Blue Pōpō Syndrome

Anter

• He aha ke kumu o ka maʻi pēpē polū?
• ʻO Tetralogy o Fallot (TOF)
• Methemoglobinemia
• Nā kīnā naʻau hānau ʻē aʻe
• He aha nā hōʻailona?
• Pehea ia ʻike?
• Pehea e mālama ʻia ai?
• Pehea e hiki ai iaʻu ke pale aku i ka maʻi polū pēpē polū?
• He aha ka manaʻo no nā pēpē me kēia ʻano?

Hōʻike Overview

ʻO ka maʻi pēpē polū kahi kūlana i hānau ʻia ai kekahi pēpē me a i ʻole ke hoʻomohala ʻana i ke kakahiaka nui. Hoʻohālikelike ʻia e ke kala o ka ʻili laulā me kahi aniani polū a poni paha, i kapa ʻia ʻo cyanosis.

Hoʻomaopopo loa ʻia kēia hiʻohiʻona bluish kahi lahilahi o ka ʻili, e like me nā lehelehe, earlobes, a me nā moena kui. ʻO ka maʻi pēpē polū, ʻoiai ʻaʻole maʻamau, hiki ke hana ma muli o kekahi mau hānau (ʻo ia hoʻi i ka wā hānau) nā kīnā o ka puʻuwai a i ʻole nā ​​kūlohelohe a i ʻole nā ​​ʻikepili.

He aha ke kumu o ka maʻi pēpē polū?

Lawe ka pēpē i kahi hue bluish ma muli o ke koko maikaʻi ʻole o oxygen. ʻO ka maʻamau, hoʻokahe ʻia ke koko mai ka puʻuwai a i nā akemāmā, kahi e loaʻa ai ka oxygen. Hoʻopiʻi ʻia ke koko i loko o ka puʻuwai a laila a puni ke kino.

Ke loaʻa ka pilikia me ka puʻuwai, nā mumū, a me ke koko paha, ʻaʻole paha e oxygenated pono ke koko. Kuhi kēia i ka ʻili e lawe i kahi kala polū. Hiki i ka nele o ka oxygenation ke kumu no kekahi mau kumu.

ʻO Tetralogy o Fallot (TOF)

ʻOiai he kīnā ʻole o ka naʻau congenital, TOF kahi kumu nui o ka maʻi polū pēpē polū. He hui maoli ia o ʻehā mau kīnā o ka puʻuwai e hiki ke hōʻemi i ke kahe o ke koko i nā akemāmā a ʻae i ke kahe oxygen-maikaʻi ʻole e kahe i loko o ke kino.

Hoʻokomo ʻia ʻo TOF i nā kūlana e like me ka loaʻa ʻana o ka lua i ka paia e hoʻokaʻawale ai i ka ventricle hema a me ka ʻākau a me kahi mākala e kahe ana i ke kahe o ke koko mai ka ventricle ʻākau i loko o ka pulmonary, a i ʻole ka lolo.

Methemoglobinemia

Loaʻa kēia ʻano mai ka lāʻau make nitrate. Hiki iā ia ke hana i nā pēpē i hānai ʻia i ke ʻano pēpē i kāwili ʻia me ka wai luawai a i ʻole nā ​​meaʻai pēpē homemade i hana ʻia me nā meaʻai momona-nitrate, e like me ka milo a me nā beets.

Kū pinepine ke ʻano i nā pēpē ma lalo o 6 mau makahiki. Keia ʻōpio, ʻoi aku ka maʻalahi a me ka hoʻomohala ʻia o nā ʻōpū o nā pēpē, kahi e hoʻololi ai i ka nitrate i nitrite. I ka holo ʻana o nitrite i loko o ke kino, hoʻopuka ia i ka methemoglobin. ʻOiai he waiwai nui ka oxygen i ka methemoglobin, ʻaʻole ia e hoʻokuʻu i kēlā oxygen i ke kahe o ke koko. Hāʻawi kēia i nā pēpē me ke ʻano i kā lākou hue bluish.

Methemoglobinemia hiki i kākaʻikahi pū kekahi.

Nā kīnā naʻau hānau ʻē aʻe

Hoʻokumu nā Genetics i nā maʻi puʻuwai congenital. ʻO kahi laʻana, loaʻa pinepine nā pilikia o ka puʻuwai i nā pēpē i hānau ʻia me Down Syndrome.

ʻO nā pilikia me ke olakino makuahine, e like me ka hūnā a me ka mālama maikaʻi ʻole ʻia o ka maʻi diabetes 2, hiki ke hopena i ka pēpē e hoʻomohala i nā kīnā ʻole o ka puʻuwai.

Hoʻokumu pū ʻia kekahi mau kīnā o ka puʻuwai no ke kumu ʻole. ʻO nā hemahema puʻuwai congenital wale nō ke kumu o ka cyanosis.

He aha nā hōʻailona?

Ma waho aʻe o ke kala bluish o ka ʻili, nā ʻōuli ʻē aʻe o ka maʻi polū pēpē polū nā:

• ukiuki
• lethargy
• nā pilikia hānai
• hiki ʻole ke loaʻa kaupaona
• nā pilikia ulu
• wikiwiki ka naʻau a me ka hanu ʻana
• nā manamana a me nā manamana wāwae i paʻa ʻia

Pehea ia ʻike?

Ma waho aʻe o ka lawe ʻana i ka mōʻaukala olakino maikaʻi loa a me ka hana ʻana i kahi hoʻokolohua kino, e hana paha ka pediatrician o kāu pēpē i kekahi mau hoʻokolohua. E kōkua kēia mau hoʻokolohua i ka hoʻoholo ʻana i ke kumu o ka maʻi pēpē polū. Hiki i nā hoʻokolohua ke hoʻopili:

• hoʻāʻo koko
• umauma X-ray e nānā i nā māmā a me ka nui o ka puʻuwai
• electrocardiogram (EKG) e nānā i ka hana uila o ka puʻuwai
• echocardiogram e ʻike ai i ka anatomy o ka puʻuwai
• catheterization naʻau e nānā i nā aʻa o ka puʻuwai
• hoʻāʻo saturation oxygen e hoʻoholo ai i ka nui o ka oxygen i loko o ke koko

Pehea e mālama ʻia ai?

Kaukaʻi pili i ke kumu o ka polū pēpē maʻi. Inā hana ʻia ke ʻano e kahi kīnā o ka naʻau hānau, pono paha kāu pēpē i kahi ʻoki ma kekahi manawa.

Paipai pū ʻia ka lāʻau. Hoʻokumu ʻia kēia mau ʻōlelo aʻoaʻo i ke koʻikoʻi o ka hemahema. Hiki i nā pēpē me ka methemoglobinemia ke hoʻohuli i ke ʻano ma ka lawe ʻana i ka lāʻau i kapa ʻia he methylene blue, hiki ke hāʻawi i ka oxygen i ke koko. Pono kēia lāʻau i kahi kuhikuhi a hāʻawi pinepine ʻia ma o ka nila i hoʻokomo ʻia i loko o kahi aa.

Pehea e hiki ai iaʻu ke pale aku i ka maʻi polū pēpē polū?

ʻO kekahi mau hihia o ka polū pēpē maʻi kahi fluke o ke kūlohelohe a ʻaʻole hiki ke pale ʻia. ʻO nā mea ʻē aʻe, hiki ke alo ʻia. Nā ʻanuʻu e komo ai:

• Mai hoʻohana i ka wai maikaʻi. Mai hoʻomākaukau i ka pīpī pēpē me ka wai luawai a hāʻawi i ka wai maikaʻi i nā pēpē e inu a hiki i ka hala ʻana o 12 mau makahiki. ʻAʻole lawe ka wai paila i nā nitrates. ʻAʻole pono nā pae Nitrate i ka wai ma mua o 10 mg / L. Hiki i kāu keʻena olakino kūloko ke hāʻawi iā ʻoe i ka ʻike hou aku e pili ana i kahi e hoʻāʻo maikaʻi ai ka wai.
• Palena i nā meaʻai momona-momona. ʻO nā meaʻai e waiwai i nā nitrates e komo pū ana me broccoli, spinach, beets, a me nā kāloti. Palena i ka nui āu e hānai ai i kāu pēpē ma mua o ko 7 mau makahiki. Inā ʻoe e hana i kāu pēpē ponoʻī a pono e hoʻohana i kēia mau mea kanu, e hoʻohana i ka hau ma mua o ka mea hou.
• Hōʻalo i nā lāʻau kū ʻole i ke kānāwai, ka puhī ʻana, ka waiʻona, a me kekahi mau lāʻau i ka wā hāpai. ʻO ka pale ʻana i kēia mau mea e kōkua i ka pale ʻana i nā maʻi puʻuwai congenital. Inā loaʻa ʻoe i ka maʻi diabetes, e nānā pono ua kaohi maikaʻi ʻia a aia ʻoe ma lalo o kahi kauka.

He aha ka manaʻo no nā pēpē me kēia ʻano?

ʻO ka maʻi maʻi pēpē polū kahi maʻi maʻamau me nā kumu like ʻole. E ʻōlelo paha kāu kauka i kekahi mea mai ka mālama koke ʻana i ke ʻoki kino. Hiki ke makaʻu loa ke kaha keʻoki ke hana ʻia ma kahi keiki hānau.

Ke ʻike ʻia ke kumu a mālama maikaʻi ʻia, hiki i ka hapanui o nā keiki me ka maʻi polū pēpē ke ola i nā ola maʻamau me nā hopena olakino.