ʻO Miglustat

Anter
- Ma mua o ka lawe ʻana i miglustat,
- Hoʻokumu paha ʻo Miglustat i nā hopena ʻaoʻao. E haʻi i kāu kauka inā koʻikoʻi kekahi o kēia mau ʻōuli a mai hele aku paha:
- Hiki i kekahi o nā hopena ʻaoʻao ke koʻikoʻi. ʻAʻole ʻike ʻia nā ʻōuli aʻe, akā inā ʻike ʻoe i kekahi o ia mau mea, e kāhea koke i kāu kauka:
- Pākuʻi ʻia paha nā ʻōuli o ka overdose:
Hoʻohana ʻia ʻo Miglustat e mālama i ka maʻi ʻo Gaucher ʻano 1 (kahi ʻano i wāwahi ʻole ʻia ai kekahi mea momona i loko o ke kino a kūkulu ʻia i loko o kekahi mau lālā a hana i nā pilikia o ke ake, nā ʻelala, nā iwi, a me nā koko). Aia ʻo Miglustat i loko o ka papa o nā lāʻau i kapa ʻia ʻo nā mea kūpale kino. Hana ia ma ka pale ʻana i ke kino mai ka hana ʻana i ka momona momona i mea e ʻemi ai ka liʻiliʻi o ia mea i ke kino a hana i nā ʻōuli.
Hele mai ʻo Miglustat ma ke ʻano he capsule e lawe ma ka waha. Lawe pinepine ʻia me ka ʻai ʻole a me ka nui o ka wai a i ʻekolu mau manawa o ka lā. E kōkua iā ʻoe e hoʻomanaʻo e lawe i ka miglustat, e lawe ma kahi o ka manawa like (s) i kēlā me kēia lā. E hāhai pono i nā ʻōkuhi i kāu lepili kuhikuhi, a nīnau i kāu kauka a kauka paha e wehewehe i kahi ʻāpana āu i maopopo ʻole ai. Lawe pono i ka miglustat e like me ke kuhikuhi. Mai lawe i ka mea ʻoi aku a liʻiliʻi paha o ia mea a lawe pinepine iā ia ma mua o ka mea i kauoha ʻia e kāu kauka.
E ale i nā capsule holoʻokoʻa; mai hoʻokaʻawale, a nau aku, a hoka ʻole iā lākou.
Mālama ʻo Miglustat i ka maʻi Gaucher akā ʻaʻole ia e hoʻōla iā ia. E hoʻomau i ka lawe miglustat ʻoiai ʻoe e ʻoluʻolu. Mai hōʻoki i ka lawe ʻana i ka miglustat me ke kamaʻilio ʻole ʻana me kāu kauka.
Kau ʻia kēia lāʻau no nā hoʻohana ʻē aʻe; e noi i kāu kauka a kauka paha no ka ʻike hou aku.
Ma mua o ka lawe ʻana i miglustat,
- e haʻi i kāu kauka a me ka kauka inā he maʻi ʻoe i ka miglustat, nā lāʻau ʻē aʻe, a me nā huahana soy.
- e haʻi i kāu kauka a me ka mea kauka lāʻau he aha nā lāʻau lapaʻau a me nā lāʻau ʻole i kuhikuhi ʻia, nā wikamina, nā mea hoʻowaiwai a me nā huahana lāʻau āu e lawe nei. E haʻi pono i ka imiglucerase (Cerezyme). Pono paha kāu kauka e hoʻololi i nā kaha o kāu mau lāʻau a nānā pono iā ʻoe no nā hopena ʻaoʻao.
- e haʻi i kāu kauka inā loaʻa iā ʻoe a i ʻole loaʻa i kahi haʻalulu (lulu ʻana i kou mau lima ʻaʻole hiki iā ʻoe ke kaohi); ʻeha, puhi, ʻā, a mū ʻole i kou mau lima a me kou mau wāwae; nā maʻi e hoʻopili i kou ʻōnaehana a maʻi maʻi ʻōpae paha.
- e haʻi i kāu kauka inā hāpai ʻoe, hoʻolālā e hāpai, a i ʻole e hānai umauma ana. Pono ʻoe e hoʻohana i ka kaohi hānau kūpono e pale i ka hāpai ʻana ʻoiai ʻoe e lawe i ka miglustat. Inā hāpai ʻoe i ka lawe ʻana i miglustat, e kāhea koke i kāu kauka. Hoʻopilikia paha ʻo Miglustat i ka fetus.
- pono ʻoe e ʻike i ka miglustat e hōʻino ai i ka sperm. Pono nā kāne e lawe ana i ka miglustat e hoʻohana i ka kaohi hānau kūpono i ka wā o ka mālama ʻana a no 3 mau mahina ma hope.
Hiki i ka Miglustat ke kumu i ka palahī a me ka pohō kaumaha. Inā ʻoe e ʻike i kēia mau hopena ʻaoʻao, e haʻi ke kauka iā ʻoe pehea e hoʻololi ai i kāu papaʻai e hoʻomaikaʻi ai i kāu mau ʻōuli. ʻ toldlelo ʻia aku paha ʻoe iā ʻoe e hōʻalo i nā mea ʻai i kiʻekiʻe i nā haʻuki. E hāhai pono i kēia mau ʻōkuhi.
E haʻalele i ka lāʻau i haʻalele ʻia a hoʻomau i kāu papa hana maʻamau. Mai lawe i kahi lāʻau pālua e pani no kahi mea i hala.
Hoʻokumu paha ʻo Miglustat i nā hopena ʻaoʻao. E haʻi i kāu kauka inā koʻikoʻi kekahi o kēia mau ʻōuli a mai hele aku paha:
- pāhoehoe
- ʻeha ka ʻōpū a bloating paha
- ʻenekini
- nalo ʻai ʻole
- Kaumaha emi
- hoʻohuhū ʻōpū
- ka luaʻi
- kōpaʻa
- hoʻomālō
- waha maloo
- nāwaliwali
- ʻūpī mākala, ʻoi aku i nā wāwae
- ke kaumaha o nā lima a me nā wāwae
- kūmau ʻole i ka hele wāwae ʻana
- ʻeha kua
- ʻūpā
- hopohopo
- ʻeha poʻo
- pilikia pilikia hoʻomanaʻo
- paʻakikī a i ʻole kaulike menstruation (wā)
Hiki i kekahi o nā hopena ʻaoʻao ke koʻikoʻi. ʻAʻole ʻike ʻia nā ʻōuli aʻe, akā inā ʻike ʻoe i kekahi o ia mau mea, e kāhea koke i kāu kauka:
- ʻeha, puhi ʻana, numbness a i ʻole ke kani ʻana i kou mau lima, nā lima, nā wāwae, a me nā wāwae
- lulu lima ʻaʻole hiki iā ʻoe ke kāohi
- nā hoʻololi i ka hihiʻo
- paopao maʻalahi a hoʻokahe koko paha
Hoʻokumu paha ʻo Miglustat i nā hopena ʻē aʻe. Kāhea i kāu kauka inā he pilikia ʻokoʻa kāu i ka lawe ʻana i kēia lāʻau.
Inā ʻoe e ʻike i kahi hopena koʻikoʻi, e hoʻouna ʻoe a i ʻole kāu kauka i kahi hōʻike i ka papahana hōʻike ʻino a MedWatch Adverse Event Food (FDA) ma ka pūnaewele (http://www.fda.gov/Safety/MedWatch) a i ʻole kelepona. 1-800-332-1088).
E mālama i kēia lāʻau i loko o ka pahu i komo ai, pani paʻa ʻia, a ʻaʻole hiki i nā kamaliʻi. E mālama iā ia i ka mahana wela o ka lumi a ma kahi o ka wela a me ka momona (ʻaʻole i ka lua.
Pono e hoʻolei ʻia nā lāʻau i koi ʻole ʻia i nā ala kūikawā e hōʻoia i ka hiki ʻole i nā holoholona, nā keiki, a me nā poʻe ʻē aʻe ke hoʻopau iā lākou. Eia nō naʻe, ʻaʻole pono ʻoe e kaomi i kēia lāʻau i ka lua. Akā, ʻo ke ala ʻoi loa e hoʻolilo i kāu lāʻau i loko o kahi papahana hoʻihoʻi lāʻau. E kamaʻilio me kāu kauka lāʻau a kāhea paha i kāu ʻōpala a me nā hana hoʻopōʻaiapuni kūloko e aʻo e pili ana i nā papahana hoʻihoʻi i kou kaiāulu. E ʻike i ka pūnaewele palekana o kā FDA's Disposal of Medicines (http://goo.gl/c4Rm4p) no ka ʻike hou aku inā ʻaʻohe ou komo i kahi papahana hoʻihoʻi.
He mea nui e mālama i nā lāʻau āpau mai ka maka a hiki i nā keiki e like me nā ipu (e like me nā minder pill i kēlā me kēia pule a me nā mea no nā kulu maka, nā kalima, nā pākuʻi, a me nā inhalers) ʻaʻole pale keiki a hiki i nā keiki ʻōpio ke wehe maʻalahi iā lākou. No ka pale ʻana i nā keiki ʻōpio mai ka lāʻau make, laka mau i nā pāpale palekana a kau koke i ka lāʻau i kahi palekana - kahi i luna a mamao a mai ko lākou alo a hiki. http://www.upandaway.org
I ke kumu o ka overdose, e kāhea i ka helpline kaohi lāʻau make ma 1-800-222-1222. Loaʻa ka ʻike ma ka pūnaewele ma https://www.poisonhelp.org/help. Inā ua hina ka mea i hoʻomāinoino ʻia, loaʻa ka hopu ʻana, pilikia i ka hanu ʻana, a i ʻole hiki ʻole ke ala aʻe, e kāhea koke i nā lawelawe kūikawā ma 911.
Pākuʻi ʻia paha nā ʻōuli o ka overdose:
- ʻeha, puhi, ʻūlū ʻana, a i ʻole numbness i kou mau lima, nā lima, nā wāwae, a me nā wāwae
- ʻeha ka ʻāʻī, ke kuni, ke anu, a i ʻole nā hōʻailona ʻē aʻe o ka maʻi
- ʻūpā
Mālama i nā manawa āpau me kāu kauka.
Mai ʻae i kahi mea ʻē aʻe e lawe i kāu lāʻau. E nīnau i kāu kauka lāʻau i nā nīnau āu e pili ana i ka hoʻopiha hou ʻana i kāu kuhikuhi.
He mea nui iā ʻoe e mālama i kahi papa inoa i kākau ʻia a me nā lāʻau lapaʻau ʻole (over-the-counter) lāʻau āu e lawe nei, a me nā huahana e like me nā huaora, nā minelala, a i ʻole nā mea hoʻopiliʻai aʻe. Pono ʻoe e lawe i kēia papa inoa me ʻoe i kēlā me kēia manawa ke kipa ʻoe i ke kauka a i ʻole inā ʻae ʻia ʻoe i kahi haukapila. He ʻike nui nō hoʻi ia e lawe pū me ʻoe inā pilikia ʻo ka pilikia.
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