ʻO Fuchs distrophy
ʻO Fuchs (haʻi ʻia ʻo "fooks") ʻo ka dystrophy kahi maʻi o ka maka kahi e hoʻomoe mālie ai nā hunaola e uhi ana i ka ʻaoʻao o loko o ke kolo. Hoʻopili pinepine ka maʻi i nā maka ʻelua.
Hiki ke hoʻoilina ʻia ʻo Fuchs dystrophy, ʻo ia hoʻi hiki ke hoʻoiho ʻia mai nā mākua a i nā keiki. Inā loaʻa kekahi o kou mau mākua i ka maʻi, he 50% kou manawa e hoʻomohala ai i kēia ʻano.
Eia nō naʻe, hiki ke kū i ke ʻano i nā poʻe me ka ʻole o ka mōʻaukala ʻohana i ʻike ʻia o ka maʻi.
ʻOi aku ka maʻamau o ka Fuchs dystrophy i nā wahine ma mua o nā kāne. ʻAʻole ʻike ʻia nā pilikia o ka hihi ma mua o ka makahiki 50 i ka hapanui o nā hihia. Eia nō naʻe, hiki i kahi mea mālama olakino ke ʻike i nā hōʻailona o ka maʻi i nā poʻe i hoʻopilikia ʻia e ko lākou 30 a 40 paha.
Hoʻopili ka Fuchs dystrophy i ka papa lahilahi o nā hunaola e kau i ka ʻaoʻao hope o ke kola. Kōkua kēia mau pūnaewele i ka pauma i ka wai i waho o ke kō. I ka lilo ʻana o nā keena he nui, hoʻomaka ka wai e kūkulu i loko o ke kole, e hoʻoulu ana a me kahi kihi ao.
I ka wā mua, kūkulu wale paha ka wai i ka wā hiamoe, ke paʻa ka maka. Ke hele a māhuahua ka maʻi, kū paha nā pupu liʻiliʻi. Piʻi ka pā nui a haki paha. ʻO kēia ke kumu o ka ʻeha o ka maka. Hiki i ka Fuchs dystrophy ke hoʻololi i ke kinona o ke kola, e alakaʻi ana i nā pilikia ʻike hou aku.
Pākuʻi ʻia paha nā ʻōuli:
- ʻEhaʻeha maka
- ʻIke ka maka i ka mālamalama a me ka ʻōlinolino
- ʻO ka hihiʻo foggy a blur paha, i ka mua i nā kakahiaka wale nō
- Ke ʻike nei i ka ʻāne waihoʻoluʻu a puni nā kukui
- ʻO ka ʻike maka ʻino ma o ka lā
Hiki i kahi mea hoʻolako ke ʻike pono iā Fuchs dystrophy i ka wā o kahi hōʻike kukui kukui.
Nā hoʻokolohua ʻē aʻe i hana ʻia e hoʻopili ʻia:
- Pachymetry - ana i ka mānoanoa o ke kōkea
- Ninaninau microscope kikoʻī - ʻae i ka mea hāʻawi e nānā i ka papa lahilahi o nā hunaola e kau ana i ka ʻaoʻao hope o ke kola
- Hōʻike ʻike ʻike hihi
Hoʻohana ʻia nā kulu maka a i ʻole nā hamo e huki ai i ka wai mai ke kōpena e hōʻoluʻolu i nā ʻōuli o Fuchs dystrophy.
Inā hoʻomohala nā ʻeha ʻeha ma ke kornea, nā aniani hoʻopili palupalu a i ʻole ke ʻoki ʻana e hana i nā pale ma luna o nā ʻeha ke kōkua i ka hōʻemi ʻana i ka ʻeha.
ʻO ka mea hoʻōla wale no ka Fuchs dystrophy kahi kope koli.
A hiki i kēia manawa, ʻo ka ʻano maʻamau o ke kanu ʻana o ke kole e komo i ke keratoplasty. I loko o kēia kaʻina hana, wehe ʻia kahi ʻāpana puni o ke kornea, e waiho ana i kahi hāmama i mua o ka maka. Hoʻohui ʻia kahi ʻāpana kornea mai kahi mea hāʻawi kanaka i ka maka i mua o ka maka.
ʻO kahi ʻenehana hou i kapa ʻia ʻo endothelial keratoplasty (DSEK, DSAEK, a i ʻole DMEK) ua lilo i koho i makemake ʻia no nā poʻe me ka Fuchs dystrophy. I kēia kaʻina hana, ua hoʻololi wale ʻia nā papa o loko o ke kornea, ma kahi o nā papa āpau. ʻO kēia ke alakaʻi i kahi wikiwiki wikiwiki a me nā pilikia liʻiliʻi. ʻAʻole pono nā kuʻi.
ʻOi aku ka maikaʻi o ka Ftrs dystrophy i ka hala ʻana o ka manawa. Me ka ʻole o ke koli ʻana, hiki i kahi kanaka me ka Fuchs distrophy koʻikoʻi e makapō a i ʻole ʻehaʻeha a hoʻoliʻiliʻi loa i ka ʻike.
ʻO nā hihia liʻiliʻi o Fuchs dystrophy e māhuahua pinepine ana ma hope o ke kaha ʻana o ka cataract. E loiloi kahi kaukō lōkō i kēia pilikia a hiki paha ke hoʻololi i ka ʻenehana a i ʻole ka manawa o kāu ʻoki cataract.
Kāhea i kāu mea hāʻawi inā loaʻa iā ʻoe:
- ʻEhaʻeha maka
- ʻIke ka maka i ka mālam
- ʻO ka manaʻo aia kekahi mea i kou maka ke loaʻa ʻole kahi mea ma laila
- Nā pilikia e ʻike ʻia ana e like me ka ʻike ʻana i ka ʻane a i ʻole ka ʻike kapua
- ʻIke hōʻino
ʻAʻohe pale e ʻike ʻia. ʻO ka pale ʻana i ke kaha ʻana o ka cataract a i ʻole ka mālama ʻana i nā hana kūikawā i ka wā o ke kāpili cataract e hoʻopaneʻe paha i ka pono no kahi transplant corneal.
Kaʻauwai o Fuchs; ʻO ka dystrophy endothelial a Fuchs; ʻO ka Ftrs 'corneal dystrophy
Folberg R. ʻO ka maka. I: Kumar V, Abbas AK, Aster JC, eds. ʻO Robbins & Cotran Pathologic Basis o ka maʻi. 10 o ka lā. Piladelapia, PA: Elsevier; 2021: chap 29.
ʻO Patel SV. I nā hoʻokolohua hoʻokolohua ma fuchs endothelial corneal dystrophy: ka hoʻonohonoho ʻana a me nā ana hopena - ka Bowman Club Lecture 2019. ʻO BMJ Open Ophthalmology. 2019; 4 (1): e000321. PMID: 31414054 pubmed.ncbi.nlm.nih.gov/31414054/.
Rosado-Adames N, Afshari NA. Nā maʻi o ka endothelium kornea. I: Yanoff M, Duker JS, eds. Ophthalmology. 5th lā. Piladelapia, PA: Elsevier; 2019: chap 4.21.
Salemona JF. Kornea. I: Salmon JF, ed. ʻO Ophthalmology Clinical Clinical. 9th ed. Piladelapia, PA: Elsevier; 2020: chap 7.