Hōʻike mimi PBG

ʻO Porphobilinogen (PBG) kekahi o nā ʻano porphyrins i loaʻa i loko o kou kino. Kōkua ʻo Porphyrins i nā mea nui i loko o ke kino. ʻO kekahi o kēia he hemoglobin, ka protein i loko o nā hunaola ʻulaʻula e lawe i ka oxygen i loko o ke koko. Haʻalele pinepine nā porphyrins i kou kino ma o ka mimi a i ʻole nā ​​noho. Inā kū ʻole kēia hana, hiki i nā porphyrins e like me PBG ke kūkulu i loko o kou kino.

Hōʻike kēia ʻatikala i ka hoʻokolohua e ana i ka nui o PBG i kahi mimi.

Ma hope o kou hāʻawi ʻana i kahi laʻana mimi, ua hoʻāʻo ʻia i ka lab. Kapa ʻia kēia he laʻana mimi huikau.

Inā pono, e noi paha kāu mea mālama ola iā ʻoe e hōʻiliʻili i kou mimi ma ka home ma mua o 24 mau hola. Kapa ʻia kēia he laʻana mimi he 24 mau hola. E haʻi aku kāu mea hāʻawi iā ʻoe pehea e hana ai i kēia. E hahai pololei i nā ʻōkuhi.

E haʻi paha kāu mea lawelawe iā ʻoe e haʻalele no ka lawe manawa ʻana i nā lāʻau e hiki ai ke hoʻololi i nā hopena hōʻike. E pono e haʻi aku i kāu mea hoʻolako e pili ana i nā lāʻau āpau āu e lawe ai. Pākuʻi ʻia kēia mau mea:

• Nā lāʻau Antibiotics a me nā lāʻau anti-fungal
• Nā lāʻau anti-hopohopo
• Pila pale hānau
• Nā lāʻau diabetes
• Nā lāʻau ʻeha
• Nā lāʻau hoʻomoe

Mai hōʻoki i ka lawe ʻana i ka lāʻau me ka kamaʻilio mua ʻole ʻana i kāu mea hāʻawi.

Pili kēia hōʻike i ka urination maʻamau wale nō, a ʻaʻohe pilikia.

Hana ʻia kēia hōʻike inā manaʻo kāu mea lawelawe iā porphyria a i ʻole kahi maʻi ʻē aʻe e pili ana me kahi pae PBG kūpono ʻole.

No kahi laʻana mimi huikau, manaʻo ʻia kahi hopena hōʻike maikaʻi ʻole he maʻamau.

Inā hana ʻia ka hōʻike ma kahi mimi 24-hola, ʻoi aku ka emi o ke kumukūʻai maʻamau ma mua o 4 milligrams no 24 mau hola (18 micromoles no 24 mau hola).

Hiki ke loli iki nā pae waiwai maʻamau i waena o nā hale hana ʻokoʻa. Hoʻohana kekahi mau labs i nā ana like ʻole a i ʻole hoʻokolohua i nā hoʻohālikelike like ʻole. E kamaʻilio i kāu mea hāʻawi e pili ana i ke ʻano o kāu mau hopena hōʻike.

ʻO ka nui o ka PBG i hoʻonui i ka mimi ma muli o:

• Hepatitis
• Lāʻau make kēpau
• Kanesa maʻi ʻaʻai
• ʻO Porphyria (mau ʻano)

ʻAʻohe pilikia me kēia hōʻike.

Hōʻike Porphobilinogen; ʻO Porphyria - mimi; PBG

• ʻŌnaehana mimi kāne

ʻO Fuller SJ, Wiley JS. Heme biosynthesis a me kāna mau maʻi: porphyrias a me sideroblastic anemias. I: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 38.

ʻO Riley RS, ʻo McPherson RA. Ninaninau maʻamau o ka mimi. I: McPherson RA, Pincus MR, hua. ʻO kā Henry's Clinical Diagnosis a me Management e nā Laboratory Methods. 23rd Ed. St Louis, MO: Elsevier; 2017: chap 28.