Hōʻailona Nikolsky
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ʻO ka hōʻailona ʻo Nikolsky kahi ʻili e loaʻa ai kahi paheʻe o ka ʻili e heʻe ai mai nā papa o lalo ke ʻānai ʻia.
ʻO ka maʻi ka mea maʻamau o nā pēpē hānau hou a i nā keiki ʻōpio ma lalo o 5 mau makahiki. Hoʻomaka pinepine ia ma ka waha a ma ka ʻāʻī, poʻohiwi, lua lima, a ma nā wahi genital. He lethargic paha kahi keiki, huhū, a me ke kuni. Hoʻolālā paha lākou i nā palapū ʻulaʻula ʻeha ma ka ʻili, a haki maʻalahi.
ʻO nā mākua me nā hana puʻuwai pīhoihoi a i ʻole me kahi ʻōnaehana pale nawaliwali e loaʻa paha kēia hōʻailona. Hiki i kāu mea mālama ola ke hoʻohana i kahi peni holoi penikala a i ʻole ka manamana lima e hoʻāʻo ai no ka hōʻailona Nikolsky. Huki ʻia ka ʻili i ka ʻaoʻao me ke kaomi hoʻopaʻa i ka ʻili, a i ʻole ke kaʻapuni ʻana i ka eraser i hope a i ʻole.
Inā maikaʻi ka hopena o ka hopena, e heʻe ka ʻāpana lahilahi o ka ʻili, a waiho ka ʻalani a pulu, a palupalu hoʻi.
ʻO kahi hopena maikaʻi he hōʻailona ia o kahi maʻi ʻili. Loaʻa nā kānaka me kahi hōʻailona maikaʻi i ka ʻili ākea e heʻe kūʻokoʻa mai nā papa o lalo ke ʻānai ʻia.
Hiki ke ʻike pinepine ʻia ka hōʻailona Nikolsky i ka poʻe me:
- ʻO nā kūlana blim autoimmune e like me pemphigus vulgaris
- Nā maʻi o ke koʻohune e like me ka maʻi ʻili scalded
- Nā hopena lāʻau e like me erythema multiforme
Kāhea i kāu mea hāʻawi inā ʻoe a i ʻole kāu keiki e hoʻomāhuahua i ka loosening ʻulaʻula, ʻulaʻula, a me ka maʻi ʻana o ka ʻili, kahi āu e ʻike ʻole ai i ke kumu o (e like me ka ʻā ʻana o ka ʻili).
Hiki ke koʻikoʻi nā kūlana e pili pū ana me ka hōʻailona ʻo Nikolsky. Pono e hoʻokomo i kekahi poʻe i ka haukapila. E nīnau ʻia ʻoe e pili ana i kāu mōʻaukala olakino a hāʻawi ʻia i kahi hoʻokolokolo kino.
E pili ka mālama ʻana i ke kumu o ke ʻano.
Hāʻawi ʻia ʻoe
- Fluid and antibiotics through a vein (intravenously).
- ʻO kaʻaila ʻaila e hoʻoliʻiliʻi i ka ʻeha
- Mālama ʻeha kūloko
ʻO ka hoʻōla ʻana o nā ʻili o ka ʻili ma kahi o 1 a 2 mau pule me ka ʻili ʻole.
Hōʻailona Nikolsky
Fitzpatrick JE, High WA, Kyle WL. ʻO nā pupuhi a me nā vesicle. I: Fitzpatrick JE, High WA, Kyle WL, eds. ʻO Dermatology Care Urgent: Diagnosis. Piladelapia, PA: Elsevier; 2018: chap 11.
Grayson W, Calonje E. Nā maʻi maʻi i ka ʻili. I: Calonje E, Brenn T, Lazar AJ, Billings SD, eds. ʻO McKee's Pathology o ka ʻili. 5th lā. Piladelapia, PA: Elsevier; 2020: chap 18.
ʻO Marco CA. Hōʻike dermatologic. I: Nā paia RM, Hockberger RS, Gausche-Hill M, nā ʻaoʻao. ʻO Rosen's Emergency Medicine: Nā Manaʻo Manaʻo a me ka hana lapaʻau. 9th ed. Piladelapia, PA: Elsevier; 2018: chap 110.