ʻO Tetralogy o Fallot

ʻO Tetralogy o Fallot kahi ʻano kīnā o ka naʻau hānau. ʻO ia hoʻi ʻo Congenital aia ia ma ka wā hānau.

Hoʻokumu ke Tetralogy o Fallot i nā pae oxygen haʻahaʻa i ke koko. Ke alakaʻi nei kēia i ka cyanosis (kahi ʻulaʻula polū i ka ʻili).

Loaʻa i ka palapala ʻano ʻehā mau kīnā o ka puʻuwai a me nā kīʻaha koko nui:

• Ventricular septal hemahema (puka ma waena o ka ventricle ʻākau a hema)
• Pahu o ka pulmonary outflow tract (ke kiwikā a me nā aʻa e hoʻopili i ka puʻuwai me nā akemāmā)
• Overriding aorta (ke aʻa e lawe i ke koko waiwai-oxygen i ke kino) i hoʻoneʻe ʻia ma luna o ka ventricle ʻākau a me nā kīnā septal ventricular, ma kahi o ka puka ʻana mai ka ventricle hema wale nō.
• Ka mānoanoa o ka paia o ka ventricle ʻākau (hypertrophy ventricular ʻākau)

Kākaʻikahi ka Tetralogy o Fallot, akā ʻo ia ka ʻano maʻamau o nā maʻi puʻuwai cyanotic congenital. Kū like ia e like me ka pinepine i nā kāne a me nā wahine. ʻO ka poʻe me ka tetralogy o Fallot e loaʻa paha i nā kīnā hānau ʻē aʻe.

ʻO ke kumu o ka nui o nā kīnā o ka naʻau congenital ʻaʻole ʻike ʻia. Pili nā kumu he nui i pili.

Nā mea e hoʻonui ai i ka makaʻu no kēia ʻano i ka wā hāpai.

• ʻAlekohola i ka makuahine
• Diabetes
• ʻO ka makuahine ma mua o 40 mau makahiki
• Kaʻai maikaʻi ʻole i ka wā hāpai
• ʻO Rubella a i ʻole nā ​​maʻi viral i ka wā hāpai

ʻO nā keiki me ka tetralogy o Fallot ka mea i loaʻa i nā maʻi chromosome, e like me Down syndrome, Alagille syndrome, a me DiGeorge syndrome (kahi ʻano e hoʻopilikia i ka naʻau, nā pae calcium liʻiliʻi, a me nā hana pale maikaʻi ʻole.

ʻO nā hōʻailona me:

• ʻO ka waihoʻoluʻu polū i ka ʻili (cyanosis), kahi e ʻinoʻino ke huhū ka pēpē
• Ka hoʻopili ʻana i nā manamana lima (ka ʻili a hoʻonui paha o ka iwi a puni nā manamana lima)
• ʻO ka hānai paʻakikī (nā ʻano hānai hānai maikaʻi ʻole)
• ʻO ka loaʻa ʻole o ke kaupaona
• Ka hala ʻana
• Hoʻolālā maikaʻi ʻole
• ʻO ka squatting i nā manawa o ka cyanosis

ʻO kahi hoʻokolohua kino me kahi stethoscope kokoke e hōʻike mau i kahi ʻōhumu o ka puʻuwai.

E komo pū paha nā hoʻāʻo:

• Pākuʻi x-ray
• Helu piha koko (CBC)
• ʻEchocardiogram
• Electrocardiogram (ECG)
• MRI o ka puʻuwai (ma hope o ke kahakaha ʻana)
• CT o ka puʻuwai

Hana ʻia ke ʻoki no ka hoʻoponopono ʻana i ka tetralogy o Fallot i ka wā ʻōpio o ke pēpē, ma mua o 6 mau makahiki o kou makahiki. I kekahi manawa, ʻoi aku ma mua o hoʻokahi kauka e pono ai. Ke hoʻohana ʻia ʻoi aku ma mua o hoʻokahi o ke kaha, hana ka ʻoki mua e kōkua i ka hoʻonui ʻana i ke kahe o ke koko i nā akemāmā.

ʻO ke ʻoki kino e hoʻoponopono ai i ka pilikia e hana ʻia ma kahi hope aku. Hoʻokahi wale nō hana ʻoki hoʻoponopono i hana ʻia i nā mahina mua o ke ola. Hana ʻia ke kaha pololei e hoʻonui i kahi ʻāpana o ka tract pulmonary liʻiliʻi a pani i ka hemahema septal ventricular me kahi patch.

ʻO ka hapa nui o nā hihia hiki ke hoʻoponopono me ke ʻoki. Hana maikaʻi nā pēpē i loaʻa i ke kāpili. Ma mua o 90% ola i ke oʻo makua a ola i ka hana, ke olakino, a me nā huahana kūpono. Me ka ʻole o ke kaha ʻana, make pinepine ka make i ka manawa a ke kanaka i hiki ai i 20 mau makahiki.

ʻO ka poʻe i hoʻomau aku, ka nui o ka leakiness o ka pulmonary valve e pono ai e pani i ka valve.

Paipai nui ʻia ka ukali pinepine ʻana me ka poʻe cardiologist.

Komo pū nā pilikia:

• Hoʻoneʻe ka ulu a me ka hoʻomohala
• Nā ritme puʻuwai ʻole kaulike (arrhythmia)
• ʻO ka hopu ʻana i nā wā ke lawa ʻole ka oxygen
• ʻO ka make mai ka hopu ʻia o ka puʻuwai, ʻoiai ma hope o ka hoʻoponopono ʻana

Kāhea i kāu mea mālama ola inā e ulu nā hōʻailona hou ʻole i wehewehe ʻia a i ʻole ke loaʻa i kahi keiki kahi ʻāpana o cyanosis (ʻili polū).

Inā lilo i keiki me ka tetralogy o Fallot i polū, kau koke i ke keiki ma ko lākou ʻaoʻao a i hope paha a kau i nā kuli i ka umauma. E hōʻoluʻolu i ke keiki a ʻimi koke i ka lāʻau.

ʻAʻohe ala i ʻike ʻia e pale ai i ke ʻano.

Tet; TOF; Hewa puʻuwai hānau - tetralogy; Maʻi naʻau cyanotic - tetralogy; Hānau hānau - tetralogy

• ʻOki puʻuwai Pediatric - hoʻokuʻu

• Puʻuwai - ʻāpana ma waena o ka waena
• ʻO Tetralogy o Fallot
• ʻO Cyanotic 'Spell spell'

ʻO Bernstein D. Cyanotic maʻi puʻuwai congenital: loiloi i ka neonate maʻi nui me ka cyanosis a me ka hanu hanu. I loko o: Kliegman RM, Stanton BF, St Geme JW, Schor NF, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21th hua. Piladelapia, PA: Elsevier; 2019: chap 456.

Fraser CD, Kane LC. Maʻi maʻi ʻōpū. I: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. ʻO Sabiston Textbook of Surgery: Ke kumu kumu olaola o ka hana ʻoki ʻana o kēia ao. 20 ouk. Piladelapia, PA: Elsevier; 2017: chap 58.

Webb GD, Smallhorn JF, Therrien J, Redington AN. ʻO ka maʻi puʻuwai Congenital i ke kanaka makua a me ka mea maʻi pediatric. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 75.