ʻO Pityriasis rubra pilaris

ʻO Pityriasis rubra pilaris (PRP) kahi maʻi ʻili laha ʻole e hiki ai i ka mumū a me ka unahi ʻana (exfoliation) o ka ʻili.

Aia kekahi mau subtypes o PRP. ʻAʻole maopopo ke kumu, ʻoiai e hoʻopili ʻia nā kumu kūlohelohe a me ka pane pale ʻole kino ʻole. Hoʻokahi subtype i pili me HIV / AIDS.

ʻO PRP kahi ʻano ʻili mau kahi e ulu ai ka ʻalani a i ʻole nā ​​salmon kala kala me ka ʻili mānoanoa ma nā lima a me nā wāwae.

E uhi paha nā wahi scaly i ka hapa nui o ke kino. ʻIke ʻia nā mokupuni liʻiliʻi o ka ʻili maʻamau (i kapa ʻia ʻo nā mokupuni ʻo sparing) i loko o nā wahi o ka ʻili unahi. ʻEwili paha nā wahi scaly. Hiki paha i nā hoʻololi i nā kui.

Hiki i PRP ke koʻikoʻi. ʻOiai ʻaʻole ia he mea hoʻoweliweli i ke ola, hiki i ka PRP ke hōʻemi nui i ka maikaʻi o ke ola a kaohi i nā hana o ka nohona o kēlā me kēia lā.

E nānā ka mea mālama ola i kou ʻili. Hana pinepine ʻia ka diagnostical e ke alo o nā ʻili ʻili ʻokoʻa. (ʻO kahi leona kahi ʻāpana ʻokoʻa ma ka ʻili). Lawe paha ka mea hāʻawi i nā laʻana (biopsies) o ka ʻili i hoʻopili ʻia e hōʻoia i ka ʻike a kāpae i nā kūlana e like paha me PRP.

Hiki ke kōkua i nā kalima kumuhana e loaʻa ana ka urea, acid lactic, retinoids, a me nā steroid. ʻO ka mea maʻamau, hoʻopili ʻia ka mālama ʻana i nā huaale i lawe ʻia e ka waha e like me isotretinoin, acitretin, a i ʻole methotrexate. Hiki ke kōkua i ka hōʻike ʻana i nā kukui ultraviolet (light therapy). Ke aʻo ʻia nei nā lāʻau e hoʻopili i ka ʻōnaehana pale o ke kino a e kūpono paha no PRP.

Hiki i kēia kumuwaiwai ke hāʻawi i ka ʻikepili hou aʻe ma PRP:

• National Organization for Rare Disorder - rarediseases.org/rare-diseases/pityriasis-rubra-pilaris

Kāhea i kāu mea hāʻawi inā hoʻomohala ʻoe i nā ʻōuli o PRP. E kāhea aku hoʻi inā loaʻa ʻoe i ka maʻi a hōʻeha nā ʻōuli.

PRP; Pityriasis pilaris; Lichen ruber acuminatus; Maʻi Devergie

• ʻO Pityriasis rubra pilaris ma ka umauma
• ʻO Pityriasis rubra pilaris ma nā wāwae
• ʻO Pityriasis rubra pilaris ma nā pāma
• ʻO Pityriasis rubra pilaris - kokoke loa

James WD, Elston DM, Hana iā JR, Rosenbach MA, Neuhaus IM. Pityriasis rosea, pityriasis rubra pilaris, a me nā maʻi papulosquamous a me hyperkeratotic. I: James WD, Elston DM, mālama iā JR, Rosenbach MA, Neuhaus IM, eds. Nā maʻi o Andrews 'o ka ʻili: Dermatology Haumāna. 13th ed. Piladelapia, PA: Elsevier; 2020: chap 11.

Patterson JW. Nā maʻi o ka pigmentation. I: Patterson JW, hoʻoponopono. ʻO Weedon's Skin Pathology. ʻEhā ed. Piladelapia, PA: Elsevier Churchill Livingstone; 2016: chap 10.