IgA vasculitis - Henoch-Schönlein purpura

ʻO IgA vasculitis kahi maʻi e pili ana i nā kiko poni ma ka ʻili, ʻeha pū, nā pilikia o ka gastrointestinal, a me ka glomerulonephritis (kahi ʻano maʻi maʻi ʻōpū). ʻIke ʻia ʻo ia ʻo Henoch-Schönlein purpura (HSP).

Hoʻokumu ʻia ka IgA vasculitis e kahi pane maʻamau o ka ʻōnaehana pale. ʻO ka hopena he mumū i loko o nā kīʻaha koko microscopic i ka ʻili. Hiki ke hoʻopili ʻia nā kīʻaha koko i nā hono, nā puʻupaʻa, a me nā ʻōpū. ʻAʻole maopopo i ke kumu o kēia hana.

ʻIke ʻia ka maʻi maʻi i nā keiki ma waena o nā makahiki 3 a me 15, akā ʻike ʻia paha i ka poʻe mākua. ʻOi aku ka maʻamau i nā keikikāne ma mua o nā kaikamahine. Nui nā poʻe i hoʻomohala i kēia maʻi i loaʻa i ka maʻi hanu luna i nā pule ma mua.

Pākuʻi ʻia paha nā ʻōuli a me nā hiʻohiʻona o IgA vasculitis:

• ʻO nā kiko poni ma ka ʻili (purpura). Kū kēia i kokoke i nā keiki āpau me ke ʻano. Kū pinepine kēia ma luna o ka pupu, nā wāwae lalo, a me nā kuʻe lima.
• Abdominal eha.
• ʻEha hui.
• Mimi maʻamau (ʻaʻohe paha ʻōuli).
• Pohā, he koko kekahi manawa.
• ʻO Hives a angioedema paha.
• ʻO Nusea a me ka luaʻi.
• ʻO ka pupuhi a me kaʻeha i ka scrotum o nā keikikāne.
• ʻEha poʻo.

E nānā ka mea mālama ola i kou kino a nānā i kou ʻili. E hōʻike ka hoʻokolohua kino i nā ʻeha o ka ʻili (purpura, lesions) a me ka palupalu pū.

E komo pū paha nā hoʻāʻo:

• Pono e hana i ka urinalysis i nā hihia āpau.
• Helu piha koko. Hiki ke maʻamau ke platelet.
• Nā hoʻāʻo hoʻohuihui: pono kēia i maʻamau.
• ʻO ka biopsy ʻili, keu hoʻi i nā mākua.
• Nānā i nā kīʻaha koko e nānā no nā kumu ʻē aʻe o ka mumū o ke kīʻaha koko, e like me ka systemus lupus erythematosus, ANCA-pili vasculitis a i ʻole hepatitis.
• I nā mākua, pono e hana i kahi biopsy hakuʻala.
• Nā hoʻokolohua kiʻi o ka ʻōpū inā ʻeha ka ʻeha.

ʻAʻohe mālama kūikawā. Hele ka hapa nui o nā hihia iā lākou iho. E hoʻomaikaʻi paha ka ʻeha hui pū me nā NSAID e like me naproxen. Inā hele ʻole nā ​​ʻōuli, kuhikuhi ʻia ʻoe i ka lāʻau corticosteroid e like me prednisone.

ʻOi aku ka maikaʻi o ka maʻi ma o kāna iho. ʻElua hapakolu o nā keiki me ka IgA vasculitis i hoʻokahi wale nō ʻāpana. Hoʻokahi hapakolu o nā keiki i loaʻa nā ʻāpana hou aʻe. Pono nā kānaka e ukali kokoke i ka olakino no 6 mau mahina ma hope o nā hanana e nānā i nā hōʻailona o ka maʻi puʻupaʻa. ʻOi aku ka makaʻu o nā mākua i ka hoʻomohala ʻana i nā maʻi puʻupuʻu mau.

Komo pū nā pilikia:

• Kahe i loko o ke kino
• Ka pale ʻana i ka ʻōpū (i nā keiki)
  
• Nā pilikia kīwī (i nā manawa kakaikahi)

Kāhea i kāu mea hāʻawi inā:

• Hoʻolālā ʻoe i nā ʻōuli o IgA vasculitis, a kū lākou ma mua o kekahi mau lā.
• Loaʻa iā ʻoe ka mimi kala a i ʻole ka hopena mimi haʻahaʻa ma hope o kahi hanana.

Immunoglobulin A vasculitis; Leukocytoclastic vasculitis; Henoch-Schönlein purpura; HSP

• ʻO Henoch-Schonlein purpura ma nā wāwae lalo
• ʻO Henoch-Schonlein purpura
• ʻO Henoch-Schonlein purpura
• ʻO Henoch-Schonlein purpura
• ʻO Henoch-Schonlein purpura ma ka wāwae o kahi pēpē
• ʻO Henoch-Schonlein purpura ma nā wāwae o ke pēpē
• ʻO Henoch-Schonlein purpura ma nā wāwae o ke pēpē
• ʻO Henoch-Schonlein purpura ma nā wāwae

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Sunderkötter CH, Zelger B, Chen KR, et al. Nomenclature o vutanculitis cutaneus: Dermatologic addendum i ka makahiki 2012 ua hoʻoponopono hou ʻia ka International Chapel Hill Consensus Conference Nomenclature o Vasculitides. Rumatika rumitis. 2018; 70 (2): 171-184. PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340.