Fibrosis pulmonary Idiopathic

Idiopathic pulmonary fibrosis (IPF) ke wili nei a i ʻole manoanoa o nā akemāme me ke kumu ʻole i ʻike ʻia.

ʻAʻole ʻike ka poʻe lawelawe olakino i ke kumu o ka IPF a no ke aha e hoʻomohala ai kekahi poʻe iā ia. ʻO ka manaʻo Idiopathic ʻaʻole ʻike ʻia ke kumu. ʻO ke kūlana ma muli paha o ka pane ʻana o nā māmā i kahi mea i ʻike ʻole ʻia a i ʻole ʻeha. He pāʻani paha kā Genes i ka hoʻomohala ʻana iā IPF. Kū pinepine ka maʻi i nā poʻe ma waena o 60 a 70 mau makahiki. ʻOi aku ka maʻamau o ka IPF i nā kāne ma mua o ka wahine.

Ke loaʻa iā ʻoe ka IPF, hele a maʻahi kou mau māmā. Hana paʻakikī kēia iā ʻoe e hanu. I ka hapanui o ka poʻe, ʻoi aku ka maikaʻi o ka IPF i nā mahina a i kekahi mau makahiki. I kekahi, ʻoi aku ka maikaʻi o ka IPF ma kahi o kahi manawa lōʻihi.

Pākuʻi ʻia paha nā ʻōuli i kekahi o kēia mau mea:

• ʻEhaʻeha umauma (kekahi manawa)
• Cough (maʻamau maloʻo)
• ʻAʻole hiki ke ʻeleu e like me ma mua
• Ka hanu ʻana o ka hanu i ka wā o ka hana (mau kēia mau ʻōuli no nā mahina a i ʻole mau makahiki, a ma kahi o ka manawa e hana ʻia ke hoʻomaha ʻia)
• Maule ka manaʻo
• ʻO ka hoʻemi hele mālie

E hana ka mea hāʻawi i kahi hoʻokolohua kino a nīnau e pili ana i kāu moʻolelo olakino. E nīnau ʻia ʻoe inā ua hōʻike ʻia ʻoe i ka asbestos a i ʻole nā ​​toxins ʻē aʻe a inā ʻoe i puhi puhi.

Loaʻa paha i ka hoʻokolohua kino loaʻa iā ʻoe:

• Kani ka hanu maʻamau i kapa ʻia he crackles
• ʻO ka ʻili Bluish (cyanosis) a puni ka waha a i ʻole nā ​​manamana lima ma muli o ka oxygen haʻahaʻa (me ka maʻi kiʻekiʻe)
• Ka hoʻonui a me ke kuhi ʻana o nā kumu manamana, i kapa ʻia ʻo clubbing (me ka maʻi kiʻekiʻe)

ʻO nā hoʻokolohua e kōkua i ke kuhi IPF e hoʻopili i kēia mau mea:

• ʻO Bronchoscopy
• ʻO ka CT scan pahu umauma kiʻekiʻe (HRCT)
• Pākuʻi x-ray
• ʻEchocardiogram
• Nā ana o ke kiʻekiʻe o ka oxygen oxygen (nā kinoea arterial)
• Nā hoʻāʻo hana pulmonary
• Hōʻoia hele hele wāwae he 6 mau minuke
• ʻO nā hoʻāʻo ʻana no nā maʻi autoimmune e like me rheumatoid arthritis, lupus, a scleroderma paha
• Open lung (ʻoki kino) lung biopsy

ʻAʻohe lāʻau i ʻike ʻia no IPF.

Hoʻolālā ʻia ka mālama ʻana i ka hoʻomaha ʻana i nā ʻōuli a me ka lohi o ka holo ʻana o ka maʻi.

• ʻO Pirfenidone (Esbriet) a me nintedanib (Ofev) ʻelua mau lāʻau lapaʻau e mālama iā IPF. Hiki iā lākou ke kōkua i ka hoʻolōʻihi i nā hōʻino o ka māmā.
• ʻO ka poʻe me ka pae haʻahaʻa o ke koko e pono i ke kākoʻo oxygen ma ka home.
• ʻAʻole hoʻōla ka hoʻoponopono hou ʻana i ka maʻi i ka maʻi, akā hiki iā ia ke kōkua i ka poʻe e hoʻoikaika kino me ka liʻiliʻi o ka hanu ʻana.

Hiki i ka hoʻololi ʻana i ka home a me ka nohona ke kōkua i ka mālama ʻana i nā ʻōuli hanu. Inā puhi ʻoe a i ʻole kekahi ʻohana paha, ʻo kēia ka manawa e kū ai.

E noʻonoʻo ʻia kahi transplant lung no kekahi poʻe me IPF holomua.

Hiki iā ʻoe ke hoʻomāmā i ke koʻikoʻi o ka maʻi ma ke komo ʻana i kahi hui kākoʻo. ʻO ke kaʻana ʻana me nā poʻe ʻē aʻe i loaʻa nā ʻike a me nā pilikia maʻamau e hiki ke kōkua iā ʻoe e noʻonoʻo ʻole.

Hiki ke ʻike hou aku i ka ʻike a me ke kākoʻo no ka poʻe me IPF a me ko lākou mau ʻohana ma:

• Pulmonary Fibrosis Foundation - www.pulmonaryfibrosis.org/life-with-pf/support-groups
• ʻAmelika Hui Pū ʻIa ʻAmelika - www.lung.org/support-and-community/

Hiki paha i IPF ke hoʻomaikaʻi a noho paʻa paha no ka wā lōʻihi me ka ʻole o ka lāʻau. ʻOi aku ka maikaʻi o ka hapa nui o ka poʻe, ʻoiai me ka lāʻau.

Ke hele a koʻikoʻi nā hōʻailona hanu, pono ʻoe a me kāu mea lawelawe e kūkākūkā i nā mālama e hoʻolōʻihi ai i ke ola, e like me ka lawe ʻana i ka māmā Kūkākūkā pū kekahi me ka hoʻolālā mālama mua.

Pākuʻi ʻia paha nā pilikia o IPF:

• Nā kiʻekiʻena Abnormally kiʻekiʻe o nā hunaola ʻulaʻula ma muli o ka haʻahaʻa o nā pae o ka oxygen
• Pulupā naha
• ʻO ke koko kiʻekiʻe ma nā aʻa o nā akemāmā
• Hoʻoikaika hanu ʻole
• Cor pulmonale (maikaʻi ʻole ka ʻaoʻao ʻākau)
• Make

Kāhea koke i kāu mea hāʻawi inā loaʻa iā ʻoe kekahi o kēia mau mea:

• Ka hanu ʻana ʻoi aku ka paʻakikī, wikiwiki, a papala paha (ʻaʻole hiki iā ʻoe ke lawe i kahi hanu hohonu)
• E hilinaʻi i mua ke noho e hanu ʻoluʻolu
• Poʻomanaʻo poʻo pinepine
• Ka hiamoe a huikau paha
• Fiva
• ʻO ka mucus pouli ke kahe ʻoe
• ʻO nā manamana lima uliuli a ʻili paha a puni kou mau manamana lima

Idiopathic diffuse interstitial pulmonary fibrosis; IPF; Pulrosary fibrosis; Alveolitis hoʻoliʻiliʻi Cryptogenic; CFA; Fibrosing alveolitis; ʻO ka pneumonitis interstitial maʻamau; UIP

• Ke hoʻohana nei i ka oxygen ma ka home

• ʻO Spirometry
• Pāʻālua
• ʻŌnaehana hanu

Pūnaewele National Heart, Lung, a me Blood Institute. Fibrosis pulmonary Idiopathic. www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. Loaʻa iā Ianuali 13, 2020.

ʻO Raghu G, ʻo Martinez FJ. Maʻi maʻi Interstitial I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 86.

Raghu G, Rochwerg B, Zhang Y, et al. ʻO kahi alakaʻi aʻoaʻo kūikawā ATS / ERS / JRS / ALAT: ka mālama ʻana i ka fibrosis pulmonary idiopathic. Hoʻohou o ka 2011 kulekele kulekele alakaʻi. ʻO Am J Respir Crit Care Med. 2015; 192 (2): e3-e19. PMID: 26177183 pubmed.ncbi.nlm.nih.gov/26177183/.

Ryu JH, Selman M, Colby TV, King TE. Nā pneumonias interstitial Idiopathic. I: Broaddus VC, Mason RJ, Ernst JD, et al, eds. ʻO Murray a me Nadel's Textbook of Respiratory Medicine. ʻElua huaʻōlelo Piladelapia, PA: Elsevier Saunders; 2016: chap 63.

Silhan LL, Danoff SK. Nonpharmacologic therapy no fibrosis pulmonary idiopathic. I: Collard HR, Richeldi L, eds. ʻO ka maʻi maʻi ʻōpū. Piladelapia, PA: Elsevier; 2018: chap 5.