Mea Kākau: Roger Morrison
Lā O Ka Hana: 19 Kepakemapa 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
ʻO kā Tumiko Wilms: he aha ia, nā ʻōuli a me nā lāʻau - Ola Kino
ʻO kā Tumiko Wilms: he aha ia, nā ʻōuli a me nā lāʻau - Ola Kino

Anter

ʻO ka tumo a Wilms, i kapa ʻia hoʻi ʻo nephroblastoma, kahi ʻano maʻi ʻaʻai laha ʻole e pili ana i nā keiki ma waena o 2 a me 5 mau makahiki, e ʻoi pinepine ana ma 3 mau makahiki. Kuhi ʻia kēia ʻano tumo e ke komo ʻana o hoʻokahi a i ʻole nā ​​puʻupaʻa ʻelua a hiki ke ʻike ʻia ma o ka ʻike ʻia ʻana o kahi nuipaʻa paʻakikī i loko o ka ʻōpū.

Kūkulu maʻamau kēia ʻano tumo me ka ʻole o nā ʻōuli, ke ʻike ʻia ke loaʻa i nā pae holomua. ʻOiai ʻike ʻia ke nui loa ia, aia ka mālama ʻana a ʻokoʻa ke ola e like me ka pae i ʻike ʻia ai ka tumo, me kahi manawa e ola ai.

Nā hōʻailona nui

Hiki ke ulu ka ʻōpū o Wilms me ka ʻole o nā ʻōuli, eia nō naʻe, ʻike mau ka nui palpable e hōʻeha ʻole i ka ʻōpū o ke keiki, a he mea nui e lawe nā mākua i ke keiki i ka pediatrician e hana iā lākou.


ʻO nā ʻōuli ʻē aʻe i hiki ke hana ma muli o kēia ʻano he:

  • Ka nele o ka makemake;
  • ʻŌpū ʻōpū;
  • Fiva;
  • Nusea a i ʻole ka luaʻi;
  • Loaʻa ke koko i ka mimi;
  • Hoʻonui i ke kahe o ke koko;
  • Hoʻololi i ka helu hanu.

Hoʻopili pinepine ka tumo ʻo Wilms i kekahi o nā puʻupaʻa, akā naʻe, aia pū paha me kahi o nā ʻelua a i ʻole ke kuʻikahi paha i nā ʻāpana ʻē aʻe o ke keiki, hoʻonāukiuki i ka maʻi maʻi a alakaʻi i nā ʻōuli koʻikoʻi ʻoi aku, e like me ka hoʻokahe ʻana o ka maka, ka loli o ka ʻike a. paʻakikī i ka hanu ʻana.

Nā kumu kūpono

ʻAʻole i wehewehe maikaʻi ʻia nā kumu o ka tumo a Wilms, ʻaʻole maopopo ia inā paha he mau hoʻoilina hoʻoilina a me nā mea e pili ana i ke kaiaulu e like me ka makuwahine i ka wā o ka hāpai ʻana ke kumu o kēia ʻano tumo. Eia nō naʻe, pili kekahi ʻano o nā syndrome i ka hanana ʻana o ka tumo a Wilms, e like me Fraser syndrome, Perlman syndrome, Beckwith-Wiedemann syndrome a me Li-Fraumeni syndrome.


Pili kekahi o kēia mau syndrome i nā loli a me nā hoʻololi ʻana o ka moʻokūʻikahi a loaʻa kahi ʻikena kikoʻī, i kapa ʻia ʻo WT1 a me WT2, a hiki i kēia ke alakaʻi i ke ʻano o ka puʻupuʻu Wilms.

Hoʻohui ʻia, ʻoi aku ka makaʻu o nā keiki i hānau ʻia me kahi pilikia hānau i kēia ʻano tumo, e like me nā keiki me ka cryptorchidism, ʻo ia ka manawa i iho ʻole mai ai ka testicle. E ʻike i nā mea hou aʻe e pili ana i ka hana ʻana i ka cryptorchidism.

Pehea e hana ʻia ai ke kuhi

Hana ʻia ka hōʻailona mua e ka palpating ʻana i ka ʻōpū i mea e nānā ai i ka nui o ka ʻōpū, i ka hoʻohui ʻana i ka nānā ʻana i nā ʻōuli i hōʻike ʻia e ke keiki. ʻO ka maʻamau noi ka pediatrician i nā hoʻokolohua kiʻi, e like me ultrasound, ultrasound, tomography i hoʻopaʻa ʻia a me nā kiʻi resonance ʻumeʻume, e nānā ai i ke kū mai o ka tumo.

ʻOiai hiki ke hoʻomohala koke a mālie hoʻi, ʻike pinepine ʻia ka tumo ma mua o ka pili ʻana o nā mea ʻē aʻe.

Nā koho lapaʻau

Hiki ke hoʻōla ʻia ʻo Wills 'tumor ma o ka mālama kūpono ʻana, ʻo ia hoʻi ka wehe ʻana i ka puʻupaʻa i hoʻopilikia ʻia, a ukali ʻia e ka lapaʻau kōkua, i hana ʻia me chemotherapy a me radiation therapy. I ka wā o ke kaha ʻana, pono ke kauka e kālailai i nā ʻōnaehana ʻē aʻe i mea e ʻike ai i nā loli ʻē aʻe a nānā i nā metastases, ʻo ia ka wā e pāhola ai ka tumo i nā ʻāpana ʻē aʻe o ke kino.


I ke kumu o ka hōʻino ʻia o nā puʻupaʻa ʻelua, hana ʻia ka chemotherapy ma mua o ke kaha ʻana i mea e loaʻa ai ka manawa kūpono e hana pono ai kekahi o nā puʻupaʻa, me ka ʻole o ka nui o ka hōʻino. E ʻike hou aʻe e pili ana i ka chemotherapy a pehea e hana ai.

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