Nā hana a me nā hōʻailona no ADPKD

Anter

• Laau Lapaʻau
• ʻO ka ulu ʻana o ka cyst kidney
• Piʻi koko kiʻekiʻe
• Nā maʻi ʻino
• ʻEha
• ʻO kaʻai a me ka hydration
• ʻOki kino e mālama i nā pilikia
• Dialysis a i ʻole ke hoʻoliʻiliʻi hakuʻala
• Nā hoʻoponopono hoʻomaikaʻi
• ʻO ka lawe lawe ʻana

ʻO Autosomal ka maʻi polycystic kidney (ADPKD) ka maʻi maʻamau o ka maʻi polycystic kidney (PKD).

Hiki iā ia ke kumu i nā ʻano pilikia like ʻole, e like me:

• ʻeha
• kahe koko kiʻekiʻe
• hakuʻala ʻole

ʻAʻohe lāʻau lapaʻau no ADPKD i kēia manawa. Kau kauka paha i kāu kauka, nā hoʻololi o ka nohona, a me nā hana ʻē aʻe e kōkua ai e hōʻoluʻolu i nā ʻōuli a pale i nā pilikia.

E heluhelu e aʻo hou aʻe e pili ana i nā hōʻailona a me nā hoʻoponopono no APDKD.

Laau Lapaʻau

Kau kauka paha i kahi kauka lāʻau e pili ana i kāu mau ʻōuli a i ʻole nā ​​pilikia o ADPKD.

ʻO ka ulu ʻana o ka cyst kidney

I ka makahiki 2018, ua ʻae ka Food and Drug Administration (FDA) i ka lāʻau tolvaptan (Jynarque) e mālama iā ADPKD.

Kōkua kēia lāʻau i ka lohi o ka ulu ʻana o nā cist e hana ʻia me ADPKD. Mālama kēia i ka hōʻino ʻana i nā puʻupaʻa a hoʻoliʻiliʻi i ka makaʻu ʻole o ke kōkō.

Aia kahi pilikia o ka hōʻeha o ke ake a i ʻole ka launa ʻana o ka lāʻau ke lawe iā tolvaptan. Hana pū me ke kauka i loea i ke olakino olakino no ka hopena maikaʻi.

Hiki ke hoʻohana ʻia ʻo Tolvaptan i nā mākua i loaʻa:

• ke kahua 2 a i ʻole 3 mau maʻi ʻōiwi maʻa i ka hoʻomaka o ka lapaʻau ʻana
• ʻike o ka holomua maʻi maʻi

ʻO nā hopena ʻaoʻao maʻamau o tolvaptan (Jynarque) pili pū:

• ʻike hihi ʻole
• pilikia i ka hanu ʻana a i ʻole ka hanu hana ʻana
• waha maloʻo a ʻili maloʻo paha
• urination pinepine
• ʻaʻala hanu peʻa hua
• hoʻonui i ka pōloli a i ʻole ka make wai
• hoʻonui i ka urination a i ʻole ka leo o ka mimi i hoʻoheheʻe ʻia
• nausea, luaʻi, a i ʻole ʻeha o ka ʻōpū
• ka houʻu ʻana
• lilo kaumaha maopopo ʻole
• nawaliwali a luhi paha

Piʻi koko kiʻekiʻe

Hiki i ke koko kiʻekiʻe ke hāʻawi i ka holomua o ka maʻi.

Hiki i kāu kauka ke koi aku i nā loli nohona a me nā lāʻau i hiki ke mālama ʻia e like me ka angiotensin-hoʻololi i ka enzyme (ACE) a i ʻole nā ​​angiotensin II receptor blockers (ARBs) e kōkua i ka mālama ʻana i kou kahe koko

Nā maʻi ʻino

Hiki ke mālama ʻia nā maʻi urinary tract (UTIs), e like me ka maʻi ʻaʻai a ʻōpala paha, e pili ana iā ADPKD me nā lāʻau antibiotic. E koi ʻia kahi papa hana ʻoi aku ka lōʻihi inā ʻoi aku ka paʻakikī o ka maʻi ma mua o ka maʻi maʻi pākī maʻalahi.

ʻEha

Hiki i nā mālama ma luna o ka counter e like me ka acetaminophen ke kōkua i ka hōʻoluʻolu i nā ʻeha e pili pū me:

• cyst i nā puʻupaʻa
• nā maʻi maʻi
• pōhaku kīhāpai

ʻO nā lāʻau lapaʻau anti-inflammatory Nonsteroidal (NSAIDs), e like me ka ibuprofen, ʻaʻole i koi pinepine ʻia ma muli o ko lākou hiki ke hoʻopilikia i nā lāʻau kahe koko a me nā hana o ka hakuʻala.

Hiki ke hoʻohana pū ʻia nā lāʻau anti-seizure e kōkua me ka ʻeha o ka ʻeha i hoʻokumu ʻia e nā ʻino nerve. Hoʻopili kēia i ka pregabalin (Lyrica) a me ka gabapentin (Neurontin).

Inā hiki ʻole ke kāohi ʻia i ka ʻeha me kēia mau hana, noʻonoʻo paha kāu kauka i ke kau ʻana i nā lāʻau ʻeha ʻē aʻe e like me opioids. He mau hopena ʻokoʻa nā Opioids a me ka hiki no ka hilinaʻi, no laila e hana pū me kāu kauka e ʻike i ka mahele lāʻau haʻahaʻa e pono ai e mālama i kou ʻeha.

E kamaʻilio mau i kāu kauka ma mua o ka lawe ʻana i kahi ʻano lāʻau hou, e like me nā mea hōʻemi ʻeha o ka counter. Hiki paha i kekahi mea hōʻeha ʻeha a me nā lāʻau ʻino ke hoʻopōʻino i kou puʻupaʻa.

ʻO kaʻai a me ka hydration

ʻO nā mea āu e ʻai ai he hopena koʻikoʻi paha i kou olakino olakino, a me kou kaomi koko. Noho ka hydrated maikaʻi ka mea ʻokoʻa, a hiki ke kōkua i ka hele ʻana i nā pōhaku kōkō a me ka pale ʻana i nā UTI.

I mea e kōkua ai iā ʻoe e hoʻomohala i nā ʻano ʻai e kūpono i kou pono olakino, e kuhikuhi paha kāu kauka iā ʻoe i kahi dietitian. Hiki iā lākou ke kōkua iā ʻoe e aʻo i nā meaʻai e hoʻopili ai i kāu papaʻai a me nā mea e palena a hōʻole paha.

ʻO kahi laʻana, paipai paha lākou iā ʻoe e:

• palena i ka paʻakai, a i ʻole ka sodium, i kāu papaʻai e like me ka hiki ke kōkua i ka hoʻēmi ʻana i kou kaomi koko
• ʻai i nā ʻāpana liʻiliʻi o nā protein kiʻekiʻe e pale ai i kou puʻupaʻa
• hoʻemi i kāu ʻai ʻana o nā momona trans- a me nā momona i hiki iā ʻoe no ka olakino puʻuwai
• e hōʻalo i ka ʻai ʻana i ka potassium a phosphorous paha
• e kaupalena i ka inu rama

He mea nui nō hoʻi e inu i nā wai a lawa e noho hydrated maikaʻi. Ke hoʻopaʻa ʻimi nei nā kānaka noiʻi i ka hopena o ka hydration i ke ʻano.

ʻOki kino e mālama i nā pilikia

Inā hoʻomohala ʻoe i nā pilikia o ADPKD, hiki i kāu kauka ke koi aku i ke kahakaha ma ke ʻāpana o kāu hoʻolālā lapaʻau.

ʻO kahi laʻana, kauoha paha lākou i ke kahakaha ke hoʻomohala ʻoe:

• nā cist i kāu mau puʻupaʻa a i ʻole nā ​​mea ʻē aʻe e hōʻeha i ka ʻehaʻeha hiki ʻole ke mālama ʻia me nā lāʻau
• diverticulitis koʻikoʻi a i ʻole hoʻi hou, e hoʻopili ai i ka paia o kāu kolona
• kahi aneurysm lolo, kahi e hoʻopili ai i nā kīʻaha koko i kou lolo

ʻO nā ʻano o nā koho ʻoki no ADPKD me:

• Paheʻe cyst ʻoki kino. ʻAʻole hiki ke ninini ʻia nā cista maʻi i pane ʻole i ka lāʻau antibiotic i ka wai me ke kui.
• Wehe a fibergoptic-alakaʻi ʻoki kino. Hiki i kēia ke hoʻokahe i nā paia o waho o nā cist e hōʻoluʻolu i ka ʻeha.
• Ka hemo ʻana o ke kunako (nephrectomy). ʻO ka hemo ʻana o kahi ʻāpana a i ʻole nā ​​kīʻaha āpau paha i hiki ke lilo i koho ʻoi loa loa no nā cist ʻaʻole hiki ke hoʻoliʻiliʻi a lawe ʻia paha ma o nā ʻano hana ʻē aʻe.
• Wehe hapa o ke akepaʻa (hepatectomy) a i ʻole transplantation. No ka hoʻonui ʻana i ke akepaʻa a i ʻole nā ​​pilikia pili i ke ake, ʻae ʻae ʻia ka lawe ʻana i ke ake a i ʻole ke kuʻina ate.

Hiki i ke ʻoki kino ke kōkua i ka hoʻopakele ʻana i kekahi mau pilikia o ke ʻano. Eia naʻe, ʻaʻole ia e hoʻolohi i ka hoʻomohala holoʻokoʻa o ADPKD.

Dialysis a i ʻole ke hoʻoliʻiliʻi hakuʻala

Hana kāu mau puʻupaʻa i kahi hana nui e ka kānana ʻana i nā huahana neoneo a me ka nui o ka wai mai kou koko.

Inā hoʻomohala ʻoe i ka hōʻino kīhāpai, pono ʻoe i ka dialysis a i ʻole ke kuʻina kidney e ola.

ʻElua ʻano nui o ka dialysis:

• hemodialysis
• dialysis peritoneal

I ka hemodialysis, hoʻohana ʻia kahi mīkini kūwaho e kānana i kou koko ma waho o kou kino. I ka dialysis peritoneal, ua hoʻopiha kou wahi ʻōpū me ka dialysate (wai dialyzing) e kānana i kou koko i loko o kou kino.

Inā loaʻa iā ʻoe kahi transplan kidney, kahi transonter e līlī i kahi kōkō manawaleʻa maikaʻi mai kahi kanaka ʻē aʻe i kou kino. He mau makahiki paha ka lōʻihi e ʻike ai i kahi hoʻokūkū puʻuwai donor maikaʻi.

Nā hoʻoponopono hoʻomaikaʻi

Hiki i kekahi mau kōkua kōkua kōkua ke kōkua i ka hoʻohaʻahaʻa ʻana i kou kaumaha a i ʻole nā ​​pae ʻeha. Hiki ke kōkua i kēia e hōʻemi i kou kaomi koko a hoʻonui i ka maikaʻi o ke ola me ADPKD.

Nā hana i hiki ke kōkua i ke koʻikoʻi a i ʻole ka mālama ʻeha pū ʻana:

• lomilomi
• ʻākehu
• noʻonoʻo
• yoga
• tai chi

He mea nui ka hoʻomaʻamaʻa ʻana i kahi nohona olakino olakino nui no ke kōkua ʻana e hoʻokele i kou kahe koko a hoʻoikaika i ke olakino maikaʻi. ʻO kahi laʻana, e hoʻāʻo e:

• e lawa ka hiamoe
• hoʻoikaika kino mau
• pale i ka puhipaka

Kamaʻilio mau i kāu kauka ma mua o ka hoʻāʻo ʻana i kahi hōʻailona kōkua hou a i ʻole hana i nā hoʻololi nui i kou nohona. Hiki iā lākou ke kōkua iā ʻoe e aʻo inā palekana iā ʻoe ke olakino a i ʻole nā ​​loli.

Mai lawe i nā lāʻau lapaʻau a i ʻole nā ​​mea hoʻohiamini me ka kamaʻilio ʻole ʻana me kāu kauka e aʻo inā palekana lākou. Hiki i nā huahana lāʻau a me nā mea hoʻowali huaʻai ʻino ke hōʻino i kou puʻupaʻa.

ʻO ka lawe lawe ʻana

ʻOiai ʻaʻohe mea hoʻōla a ADPKD i kēia manawa, hiki i kāu kauka ke koi aku i nā lāʻau, nā lāʻau lapaʻau, nā hoʻolālā nohona, a i kekahi mau manawa, ke ʻoki e kōkua i ka mālama ʻana i ke ʻano.

E hoʻomaopopo i kāu kauka inā hoʻomohala ʻoe i nā hōʻailona hou a i ʻole nā ​​hoʻololi ʻē aʻe i kou olakino. Paipai paha lākou i nā hoʻoponopono i kāu hoʻolālā lapaʻau.

E kamaʻilio me kāu kauka e aʻo hou e pili ana i nā pono kūpono, nā pilikia, a me nā kumukūʻai o nā koho lapaʻau like ʻole.