Pehea e ʻike ai a mālama ai iā Caroli Syndrome

Anter

• Nā ʻōuli o Caroli Syndrome
• ʻO ka mālama ʻana no Caroli Syndrome

ʻO Caroli Syndrome kahi maʻi laha ʻole a hoʻoilina hoʻi e pili ana i ke ake, ka mea i loaʻa kona inoa no ka mea ʻo ia ke kauka Palani ʻo Jacques Caroli nāna i ʻike i ka makahiki 1958. He maʻi ia i hōʻike ʻia e ka dilation o nā kahawai e hāpai i ka paila, e ʻeha ana ma muli o ʻōpala. kēlā mau kahawai like. Hiki iā ia ke hana i nā cist a me ka maʻi, i ka hoʻohui me ka pili pū ʻia me ka fibrosis o ke ake, ʻo ia kekahi ʻano ʻoi loa o ka maʻi.

Nā ʻōuli o Caroli Syndrome

Hiki ke hoʻomau i kēia maʻi me ka ʻole o ka hōʻike ʻana i kekahi ʻōuli ma mua o 20 mau makahiki, akā ke hoʻomaka lākou e ʻike, hiki iā lākou ke:

• ʻEha ma ka ʻaoʻao ʻākau o ka ʻōpū;
• Fiva;
• Hoʻā ahi lehulehu;
• Ka ulu ʻana o ke ake;
• ʻO ka ʻili melemele a me nā maka.

Hiki i ka maʻi ke hōʻike i kēlā me kēia manawa i ke ola a hiki ke hoʻopili i kekahi mau lālā o ka ʻohana, akā hoʻoili ia i ka recessively, ʻo ia hoʻi he mau mea lawe ka makuakāne a me ka makuahine i ka gen i hoʻololi ʻia no ka hānau ʻana o ke keiki me kēia maʻi. ʻo ia ke kumu he kākaʻikahi loa ia.

Hiki ke hana i ke kuhi ma o nā hoʻokolohua e hōʻike ana i nā dilatations saccular o nā aʻa aʻa intrahepatic, e like me ka ultrasound ʻōpū, ka tomography helu, endoscopic retrograde cholangiopancreatography a me ka cholangiography transcholaryngeal transutanary.

ʻO ka mālama ʻana no Caroli Syndrome

Hoʻomaopopo ka mālama ʻana i ka lawe ʻana i nā lāʻau ʻaloʻalo, ke ʻoki e hemo ai nā cist inā pili ka maʻi i hoʻokahi ʻula o ke ake, a pono paha ke transplantation ate i kekahi mau hihia. ʻO ka maʻamau, pono e ukali ʻia kekahi kanaka e nā kauka no ke ola ma hope o ka ʻike ʻia.

I mea e hoʻomaikaʻi ai i ke ola o ke kanaka, koi ʻia e ukali ʻia e kahi nutristist i mea e hoʻomaʻamaʻa ai i ka papaʻai, e pale ana i ka ʻai ʻana i nā meaʻai e pono ai ka ikaika mai ke akepaʻa, ka mea waiwai i nā toxins a momona i ka momona.