Mea Kākau: Tamara Smith
Lā O Ka Hana: 27 Ianuali 2021
HōʻAno Hou I Ka Lā: 24 Iune 2024
Anonim
ʻO Bartter's Syndrome: he aha ia, nā hōʻailona nui a me ka mālama ʻana - Ola Kino
ʻO Bartter's Syndrome: he aha ia, nā hōʻailona nui a me ka mālama ʻana - Ola Kino

Anter

ʻO ka maʻi maʻi ʻo Bartter kahi maʻi laha ʻole e hoʻopili i nā puʻupaʻa a lilo i ka nalowale o ka potassium, sodium a me chlorine i ka mimi. Hoʻoemi kēia maʻi i ka paʻa o ka calcium i loko o ke koko a hoʻonui i ka hana o aldosterone a me renin, nā homone i loko o ka kaohi o ke kaʻe koko.

ʻO ke kumu o Bartter's Syndrome he genetic a he maʻi ia e hele aʻe mai nā mākua a i nā keiki, e pili ana i kēlā me kēia kanaka mai ka wā kamaliʻi. ʻAʻohe mea ola o kēia maʻi, akā inā ʻike mua ʻia, hiki ke kaohi ʻia ma o nā lāʻau a me nā mea hoʻopili mineral.

Nā hōʻailona nui

Hōʻike nā ʻōuli o Bartter's Syndrome i ka wā kamaliʻi, ʻo nā mea nui:

  • Kaʻai pono ʻole;
  • Ka hoʻohaʻahaʻa ulu ʻana;
  • Nāwaliwali o ka ʻiʻo;
  • Hoʻoiho noʻonoʻo;
  • Hoʻonui i ka nui o ka mimi;
  • Make wai loa;
  • Make wai;
  • Fiva;
  • Pohā a luaʻi paha.

Loaʻa nā poʻe me ka Bartter's Syndrome i nā pae haʻahaʻa o ka potassium, chlorine, sodium a me calcium i loko o ko lākou koko, akā ʻaʻohe o lākou loli i ke kiʻekiʻe o ke kaomi koko. Hiki paha i kekahi poʻe ke ʻano o ke kino e hōʻike ana i ka maʻi, e like me ke alo triangular, kahi lae ʻoi aku ka nui, nā maka nunui a me nā pepeiao kū i mua.


ʻO ka hōʻailona o Bartter's Syndrome i hana ʻia e ka urologist, ma o ka loiloi ʻana i nā ʻōuli o ka mea maʻi a me nā hoʻokolohua koko e ʻike i nā pae kaulike ʻole i ka hoʻoliʻiliʻi o ka potassium a me nā hormones, e like me ka aldostero a me ka renin.

Pehea e hana ai i ka lāʻau

Hana ʻia ka mālama ʻana iā Bartter's Syndrome me ka hoʻohana ʻia ʻana o nā potassium potassium a i ʻole nā ​​minelala ʻē aʻe, e like me ka magnesium a i ʻole ka calcium, e hoʻonui ai i ka nui o kēia mau mea i loko o ke koko, a me ka ʻai ʻana i nā wai he nui, e uku ana no ka lilo nui o ka wai e ka mimi.

Hoʻohana ʻia nā lāʻau diuretic e mālama i ka potassium, e like me spironolactone, i ka mālama ʻana i ka maʻi, a me nā lāʻau non-steroidal anti-inflammatory e like me indomethacin, a pono e lawe ʻia a hiki i ka hopena o ka ulu ʻana e hiki ai i ka hoʻomohala maʻamau o kēlā me kēia. .

Pono nā mea maʻi e loaʻa i ka mimi, ke koko a me nā hoʻokolohua ultrasound kidney. Mālama kēia i ka hana o nā puʻupaʻa a me nā ʻōpū o ka gastrointestinal, e pale ana i nā hopena o ka mālama ʻana i kēia mau lālā.


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