Maʻi paʻa kanaka paʻa

Anter

• Nā ʻōuli
• Lapaʻau

I ka maʻi paʻa o ke kanaka, loaʻa ka rigidity ikaika o ke kanaka i hiki ke hōʻike iā ia iho i ke kino holoʻokoʻa a i ʻole nā ​​wāwae wale nō, no ka laʻana. Ke pili kēia mau mea, hiki i ke kanaka ke hele wāwae e like me ke koa no ka mea ʻaʻole hiki iā ia ke neʻe maikaʻi i kona mau mākala a me nā hono.

ʻO kēia kahi maʻi autoimmune e hōʻike maʻamau ma waena o 40 a 50 mau makahiki o ka makahiki a ʻike ʻia ʻo Moersch-Woltmann syndrome a i ʻole ma ka ʻōlelo Pelekania, Stiff-man syndrome. Ma kahi o 5% wale nō o nā hihia i kū i ka wā kamaliʻi a ʻōpio paha.

Hiki i ke kanaka maʻi maʻi paʻa ke hōʻike i 6 mau ʻano like ʻole:

1. Ke ʻano kahiko kahi e hoʻopili ai i ka lumbar a me nā wāwae wale nō;
2. ʻAno ʻano ʻano ʻē ke kaupalena ʻia i ka 1 mau lālā wale nō me ke ʻano dystonic a i hope paha;
3. Laha ke ʻano o ka ʻoʻoleʻa ma loko o ke kino ma muli o ka encephalomyelitis autoimmune koʻikoʻi;
4. Ke loaʻa kahi maʻi o ka neʻe ʻana o ka hana;
5. Me ka dystonia a me ka parkinsonism ākea a
6. Me nā paramaresis spastic hoʻoilina.

ʻO ka mea maʻamau ʻaʻole kēia maʻi i loaʻa i kēia maʻi, akā loaʻa pū kekahi i nā maʻi autoimmune e like me ka maʻi diabetes 1, ka maʻi thyroid a i ʻole vitiligo.

Hiki ke hoʻōla ʻia kēia maʻi me ka lāʻau i hōʻike ʻia e ke kauka akā hiki ke hoʻolōʻihi i ka manawa.

Nā ʻōuli

ʻO nā ʻōuli o ka maʻi paʻa o ke kanaka koʻikoʻi a hoʻokomo pū ʻia:

• ʻO nā spasms muscle mau e pili ana i nā kuʻikahi liʻiliʻi i kekahi mau mākala me ka hiki ʻole i ka mea ke kaohi, a
• Pākuʻi ʻia i nā mākala e hiki ai ke hoʻohaunaele i nā olonā, nā dislocations a me nā iwi haʻi.

Ma muli o kēia mau hōʻailona hiki i ke kanaka ke loaʻa i ka hyperlordosis a me ka ʻeha o ka iwi kuamoo, keu hoʻi ke pili ka nā kua o hope a hāʻule pinepine no ka mea ʻaʻole hiki iā ia ke neʻe a kaulike kūpono.

Kū pinepine ka paʻakikī paʻakikī paʻakikī ma hope o ke kau o ke koʻikoʻi ma ke ʻano he hana hou a i ʻole e hana i nā hana i ka lehulehu, a ʻaʻole kū ka paʻakikī i ka wā hiamoe a me nā deformities i nā lima a me nā wāwae maʻa mau ma muli o ke kū ʻana o kēia mau spasms, inā ka ʻaʻole mālama ʻia ka maʻi.

ʻOiai ka hoʻonui ʻia o ke kani o nā mākala i nā wahi i hoʻopilikia ʻia, maʻamau nā reflexes tendon a no laila hiki ke hana i ka hōʻailona me nā hoʻokolohua koko e ʻimi nei i nā antibodies a me ka electromyography. Pono e kauoha ʻia nā X-ray, MRI a me CT scans e kāpae i ka hiki i nā maʻi ʻē aʻe.

Lapaʻau

Pono e hana i ka mālama ʻana i ke kanaka ʻoʻoleʻa me ka hoʻohana ʻana i nā lāʻau e like me baclofen, vectoruronium, immunoglobulin, gabapentin a me diazepam i hōʻike ʻia e ka neurologist. I kekahi manawa, pono paha e noho i ka ICU i mea e hōʻoia ai i ka hana kūpono o nā māmā a me ka puʻuwai i ka manawa o ka maʻi a hiki ke hoʻololi i ka manawa lapaʻau mai kekahi mau pule a i nā mahina.

Hiki ke hōʻike ʻia ka transfusion Plasma a me ka hoʻohana ʻana i anti-CD20 monoclonal antibody (rituximab) a loaʻa nā hopena maikaʻi. ʻO ka hapa nui o ka poʻe i ʻike ʻia me kēia maʻi e hoʻōla ʻia i ka loaʻa ʻana o ka lāʻau.