ʻO porphyria Cutaneous

Anter

• Nā ʻōuli o ka porphyria cutaneous
• ʻO ka mālama ʻana no porphyria cutaneous

ʻO ka porphyria ʻili lohi ka ʻano pinepine o ka porphyria e hōʻike i nā leona liʻiliʻi i ka ʻili i hōʻike ʻia i ka lā, e like me ka hope o ka lima, ka maka a i ʻole ke poʻo, ma muli o ka nele o kahi enzyme i hana ʻia e ke akepaʻa e alakaʻi i ka ka hōʻiliʻili o ka hao i ka ʻili. ke koko a me ka ʻili. ʻAʻohe lāʻau hoʻōla o Cutaneous porphyria, akā hiki ke kāohi ʻia me ka hoʻohana ʻana i nā lāʻau i kuhikuhi ʻia e ka dermatologist.

ʻO ka maʻamau, ʻike ʻia ka porphyria ʻili lohi i ka wā makua, keu hoʻi i nā mea maʻi inu pinepine i ka ʻalekiko a i ʻole nā ​​pilikia i ke ake, e like me ka hepatitis C, no ka laʻana.

ʻO ka ʻelima hope porphyria ʻaʻole ia he genetical, eia nō naʻe, i kekahi mau hihia hiki ke hele aʻe mai nā mākua a i nā keiki, a paipai ʻia ka ʻōlelo aʻoaʻo ʻaoʻao ma mua o ka hāpai ʻana, inā he nui nā hihia i ka ʻohana.

Nā ʻōuli o ka porphyria cutaneous

ʻO ka ʻōuli mua o ka porphyria cutaneous ka helehelena o nā palapū liʻiliʻi ma ka ʻili i waiho ʻia i ka lā, kahi manawa e hoʻōla ai, akā, ʻo nā ʻōuli ʻē aʻe kekahi:

• Hoʻonui ulu o ka lauoho i ka maka;
• ʻO ka ʻili paʻakikī i kekahi mau wahi, e like me nā lima a i ʻole ke alo;
• Mimi ʻeleʻele.

Ma hope o ka nalowale ʻana o nā palapū, ʻike ʻia nā scars a i ʻole nā ​​kiko uila i lōʻihi ka lōʻihi e hoʻōla ai.

ʻO ke kuhi o ka porphyria cutaneous pono e hana ʻia e kahi dermatologist ma o ke koko, mimi a me nā hoʻokolohua feces e hōʻoia i ke kū ʻana o ka porphyrin i loko o nā hunaola, no ka mea he waiwai ia i hana ʻia e ke akepaʻa i ka manawa o ka maʻi.

ʻO ka mālama ʻana no porphyria cutaneous

Pono e alakaʻi ʻia ka mālama ʻana no ka porphyria cutaneous e kahi dermatologist i ka laulima ʻana me ka hepatologist, ʻoiai he mea pono e kaohi i nā pae o ka porphyrin e hana ʻia e ke ake. No laila, kaukaʻi ʻia i nā ʻōuli o ka mea hoʻomanawanui, hiki ke hana i ka lāʻau me nā lāʻau no porphyria cutaneous, e like me chloroquine a i ʻole hydroxychloroquine, ka huki koko maʻamau e hoʻemi i nā pae hao i nā hunaola a i ʻole ka hui pū o nā mea ʻelua.

Hoʻohui ʻia, i ka wā o ka lapaʻau e koi ʻia ka mea hoʻomanawanui e hōʻalo i ka inu waiʻona a me ka puka ʻana o ka lā, ʻoiai me ka pale o ka lā, a ʻo ke ala maikaʻi loa e pale aku ai i ka ʻili mai ka lā e hoʻohana ai i nā pālule, nā wili lima lōʻihi, ka pāpale a me nā mīkina lima, no ka laʻana .