Hemochromatosis: he aha ia, nā ʻōuli a me nā lāʻau

Anter

• Nā ʻōuli o Hemochromatosis
• Pehea e hana ʻia ai ke kuhi
• Nā kumu o ka hemochromatosis
• Pehea e hana ai i ka lāʻau
• Pehea e pono ai ka meaʻai

He maʻi ʻo Hemochromatosis kahi i nui ai ka hao i loko o ke kino, e ʻoluʻolu nei i ka hōʻiliʻili ʻana o kēia mineral i loko o nā ʻāpana like ʻole o ke kino a me ke ʻano o nā pilikia e like me ka cirrhosis o ke ake, diabetes, ʻeleʻele o ka ʻili, maikaʻi ʻole ka puʻuwai, ʻeha pū. a i ʻole moe kolohe ka moe kolohe, no ka laʻana.

Hōʻike ʻia ka lapaʻau ʻana no ka hemochromatosis e ka hematologist, me nā phlebotomies, i lawe ʻia i kēlā me kēia manawa mai ke koko i hoʻohuli ʻia ai ka hao i waiho ʻia i nā hunaola ʻulaʻula hou a ke kino e hana ai, a i kekahi mau manawa ka hoʻohana ʻana o nā chelator mai ke kino e hōʻike pū ʻia. hao, ʻoiai lākou e kōkua i ka hoʻopau ʻana.

Nā ʻōuli o Hemochromatosis

Kū aʻe nā hōʻailona Hemochromatosis ke kiʻekiʻe loa nā pae o ka hao i ke koko, kahi e waiho ai ia i loko o kekahi mau mea e like me ke ake, ka puʻuwai, pancreas, ka ʻili, nā hono, nā testicle, nā ovaries, ka thyroid a me ka pituitary gland. No laila, ʻo nā hōʻailona nui a me nā hōʻailona e ala aʻe ʻo:

• Māluhiluhi;
• Nāwaliwali;
• Cirrhosis o ke ake;
• Diabetes;
• Hewa ka naʻau a me nā arrhythmia;
• ʻEha hui;
• Loaʻa ʻole o ka menstruation.

Eia hou, i kekahi mau hihia, hiki i ka hao keu ke kumu i ka impotence moekolohe, ka infertility a me ka hypothyroidism. ʻIke i nā ʻōuli ʻē aʻe e hōʻike ana i ka hao nui.

Pehea e hana ʻia ai ke kuhi

Hana mua ʻia ke kuhi o ka hemacromatosis ma o ka loiloi ʻia o nā ʻōuli a me nā hoʻokolohua koko i hōʻike ʻia e ka hematologist a i ʻole ka mea hana maʻamau i mea e loiloi ai i nā kiʻekiʻe o ka hao i loko o ke kino, me ka hoʻohui o ka ferritin a me ka transferrin saturation, e pili pū ana me ka mālama a me ka lawe ʻana i ka hao i loko o ke kino.

Hoʻohui ʻia, kauoha ʻia paha nā hoʻokolohua ʻē aʻe e kōkua i ka ʻimi ʻana i nā kumu o ka hemochromatosis, a e ʻōlelo ʻia paha kēia mau mea aʻe:

• ʻImi hoʻāʻo, ka mea e hōʻike i nā loli i nā genes i kumu i ka maʻi;
• ʻO ka biopsy ate, keu hoʻi inā ʻaʻole hiki ke hōʻoia i ka maʻi a i ʻole e hōʻoia i ka waiho hao ma ke akepaʻa;
• Hōʻike hoʻāʻo Phlebotomy, hana ʻia me ka haʻalele ʻana o ke koko a me ka nānā ʻana i nā pae hao, ke hōʻike nui ʻia nei no ka poʻe hiki ʻole ke hana i kahi biopsy ate a i ʻole kahi kānalua e pili ana i ka hōʻailona;

E hiki nō i ka hematologist ke noi i nā ana o nā akepau akepaʻa, e ʻimi i ka hana a i ʻole ka waiho o ka hao i loko o nā lālā i hiki ke hoʻopili ʻia, a me ka hoʻokaʻawale ʻana i nā maʻi ʻē aʻe i hiki ke hana i nā hōʻailona like.

Pono e nānā ʻia ʻo Hemochromatosis i ka poʻe i loaʻa nā hōʻailona kuhi, ke loaʻa ʻole ka maʻi ate, diabetes, maʻi puʻuwai, hana kīnā ʻole a i ʻole ka maʻi hui, a me nā poʻe i loaʻa ka ʻohana mua me ka maʻi a i ʻole nā ​​loli i ka helu o hoʻāʻo koko i ka hao.

Nā kumu o ka hemochromatosis

Hiki i ka Hemochromatosis ke hana ma ke ʻano he hopena o nā loli a i ʻole he hopena o nā maʻi e pili ana i ka luku ʻia o nā hunaola ʻulaʻula, kahi e hāpai ai i ka hoʻokuʻu ʻia o ka hao i loko o ke koko. No laila, e like me ke kumu, hiki ke hoʻokaʻawale ʻia ka hemochromatosis i:

• Hemochromatosis hoʻoilina, ʻo ia ke kumu nui o ka maʻi a kū ia ma muli o ka hoʻololi ʻana i nā genes ke kuleana no ka lawe ʻana o ka hao i loko o ka digestive tract, e hoʻomaka ana e komo i ka nui, e hoʻonui ana i ka nui o ka hao o ka hao i loko o ka meaola;
• Haemochromatosis ʻelua a loaʻa paha, kahi e loaʻa ai ka hōʻiliʻili o ka hao ma muli o nā hanana ʻē aʻe, ʻo ka nui hemoglobinopathies, kahi e luku ai nā hunaola ʻulaʻula i nā nui o ka hao i ke kahe o ke koko. ʻO nā kumu ʻē aʻe ke hoʻololi hou ʻana i ke koko, cirrhosis mau a hoʻohana kūpono ʻole paha o nā lāʻau anemia, no ka laʻana.

He mea nui e ʻike ʻia ke kumu o ka hemochromatosis e ke kauka, no ka mea, no laila hiki ke hōʻike ʻia ka lapaʻau kūpono loa, e kōkua ana i ka pale ʻana i nā pilikia a hoʻomāmā i nā ʻōuli i hana ʻia e ka nui o ka hao.

Pehea e hana ai i ka lāʻau

ʻAʻohe lāʻau i ka hemochromatosis hereditary, eia nō naʻe, hiki ke hana i ka lāʻau ma ke ʻano e hoʻemi i nā hale kūʻai hao i ke koko a pale i nā waiho i loko o nā ʻokena. No laila, i kēia mau hihia, ʻo ke ʻano nui o ka mālama ʻana he phlebotomy, i kapa ʻia hoʻi he kahe ʻana, kahi e lawe ʻia ai ke ʻāpana o ke koko i lilo ai ka hao nui i ʻāpana o nā hunaola ʻulaʻula hou a ke kino e hana ai.

ʻOi aku ka nui o ka hana i ka wā mua o ka hoʻomaʻamaʻa ʻana, akā pono e hana i nā kaha mālama, kahi ma kahi o 350 a 450 ml o ke koko e lawe ʻia ai 1 a 2 mau manawa i ka pule. A laila, hiki ke kaʻawale nā ​​kau e like me ka hopena o nā hoʻokolohua ukali, i hōʻike ʻia e ka hematologist.

ʻO kekahi koho lapaʻau ma o ka hoʻohana ʻana i nā lāʻau i ʻike ʻia he chelators hao a i ʻole "scavengers", e like me Desferroxamine, ke hoʻolaha nei lākou i ka hoʻoliʻiliʻi o nā pae hao e holo nei. Hōʻike ʻia kēia lāʻau no ka poʻe hiki ʻole ke hoʻomanawanui i ka phlebotomy, ʻo ia hoʻi ka poʻe me ka anemia koʻikoʻi, ka puʻuwai puʻuwai a i ʻole cirrhosis kiʻekiʻe o ke ake.

E ʻike i nā kikoʻī no ka mālama ʻana no ka hao nui ma ke koko.

Pehea e pono ai ka meaʻai

Ma waho aʻe o ka lāʻau i hōʻike ʻia e ke kauka, he mea nui nō hoʻi e hoʻolohe i ka meaʻai, a koi ʻia e hōʻalo i ka ʻai nui ʻana o nā meaʻai i ka hao. ʻO kekahi mau alakaʻi e pili ana i ka meaʻai nā:

• Hōʻalo i ka ʻai ʻana i ka ʻiʻo i ka nui, hāʻawi i ka makemake i ka ʻiʻo keʻokeʻo;
• E ʻai i ka iʻa ma ka liʻiliʻi i ʻelua mau manawa o ka pule;
• Hōʻalo i ka ʻai ʻana i nā mea kanu hao, e like me ka milo, beets a i ʻole nā ​​pīni ʻōmaʻomaʻo, ʻoi aku i hoʻokahi manawa i ka pule;
• ʻAi i ka palaoa palaoa āpau ma kahi o ka berena keʻokeʻo a i hoʻopiha ʻia i ka hao;
• ʻAi i ka tī, ka waiū a i ʻole ka yogurt i kēlā me kēia lā no ka mea e hoʻemi ka calcium i ka lawe hao ʻana;
• Hōʻalo i ka ʻai ʻana i nā hua maloʻo, e like me nā hua puaʻa, i nā nui he nui no ka mea waiwai i ka hao.

Eia kekahi, pono i ke kanaka ke pale aku i nā mea inu ʻona i mea e hōʻalo ai i ka hōʻino o ke ake a ʻaʻole e hoʻopau i nā huaora vitamina me ka hao a me ka huaora C, no ka mea hoʻonui kēia i ka lawe ʻana o ka hao.