Eisenmenger maʻi

ʻO ka maʻi ʻo Eisenmenger he ʻano ia e pili ana i ke kahe o ke koko mai ka puʻuwai a i nā akemāmā i kekahi poʻe i hānau ʻia me nā pilikia kūlohelohe o ka puʻuwai.

ʻO kahi maʻi ʻo Eisenmenger kahi hopena i hopena ʻia mai ke kahe o ke koko i hana ʻia e kahi kīnā i ka puʻuwai. ʻO ka hapanui pinepine, hānau ʻia ka poʻe me kēia ʻano me ka puka ma waena o nā keʻena pumping ʻelua - ka ventricle hema a me ka ʻākau - o ka puʻuwai (hemahema septal ventricular). ʻAe ka lua i ke koko i ʻohiʻohi i ka oxygen mai nā akemāmā e kahe hou i loko o nā māmā, ma kahi o ka hele ʻana i ke koena o ke kino.

Nā kīnā kīnā ʻole e hiki ai ke alakaʻi iā Eisenmenger maʻi pū kekahi:

• Aʻo hema o ke kahawai Atrioventricular
• Hewa septal Atrial
• Maʻi maʻi naʻau Cyanotic
• Patent ductus arteriosus
• Truncus arteriosus

I loko o nā makahiki he nui, hiki i ka hoʻonui ʻia o ke kahe o ke koko ke hōʻino i nā kīʻaha koko liʻiliʻi i nā akemāmā. ʻO kēia ke kumu o ke kiʻekiʻe o ke koko i nā akemāmā. A ʻo kahi hopena, hele hope ke kahe o ke koko ma waena o ka lua ma waena o nā keʻena pumping ʻelua. ʻAe kēia i ke koko ʻilihune o ka oxygen e hele i ke koena o ke kino.

E hoʻomaka paha ʻo Eisenmenger maʻi e hoʻomohala ma mua o ka ʻōpio ʻana o kahi keiki. Eia nō naʻe, hiki ke hoʻomohala i ka wā ʻōpio makua, a holomua paha i ka wā ʻōpio.

ʻO nā hōʻailona me:

• Nā lehelehe Bluish, nā manamana lima, nā manamana wāwae, a me ka ʻili (cyanosis)
• Nā manamana lima a me nā manamana wāwae (clubbing)
• Numbness a me ke kani ʻana o nā manamana a me nā manamana wāwae
• ʻEha ʻeha
• ʻApu ʻana i ke koko
• Puʻupuʻu
• Mauleʻa
• Luhi luhi
• Pokole o ka hanu
• Hōʻalo i nā puʻuwai (palpitations)
• Hahau
• ʻO ka pehu ʻana i nā hono i hoʻokumu ʻia e ka nui o ka uric acid (gout)

E nānā ka mea mālama ola i ke keiki. I ka wā o ka hoʻokolohua, loaʻa paha i ka mea hāʻawi:

• Rhythm puʻuwai maʻamau (arrhythmia)
• ʻO nā wēlau nui o nā manamana lima a me nā manamana wāwae (clubbing)
• ʻŌhumu ʻo Heart (kahi keu ke kani ke hoʻolohe ʻana i ka puʻuwai)

E hōʻoia ka mea hāʻawi iā Eisenmenger Syndrome e ka nānā ʻana i ka mōʻaukala o ke kanaka no nā pilikia puʻuwai. E komo pū paha nā hoʻāʻo:

• Helu piha koko (CBC)
• Pākuʻi x-ray
• MRI scan o ka puʻuwai
• Ke hoʻokomo nei i kahi paipu lahilahi i loko o ke aʻa e nānā i ka puʻuwai a me nā kīʻaha koko a ana i nā kaomi (catheterization cardiac)
• Hōʻike o ka hana uila i ka puʻuwai (electrocardiogram)
• Ultrasound o ka puʻuwai (echocardiogram)

Ua heleleʻi ka nui o nā hihia o kēia ʻano ma ʻAmelika Hui Pū ʻIa no ka mea hiki i nā kauka ke hōʻoia koke a hoʻoponopono i ka hemahema i kēia manawa. No laila, hiki ke hoʻoponopono i ka pilikia ma mua o ka hōʻino ʻole i hiki i nā aʻa māmā liʻiliʻi.

I nā manawa, hiki i ka poʻe me nā ʻōuli ke lawe i ke koko mai ke kino (phlebotomy) e hoʻemi i ka nui o nā hunaola ʻulaʻula. Lawe ʻia ke kanaka i nā wai e pani i ke koko nalowale (ka hoʻololi leo).

Loaʻa i ka poʻe i hoʻopilikia ʻia i ka oxygen, ʻoiai ʻaʻole maopopo inā kōkua ia e pale i ka maʻi mai ka ʻino loa. Hoʻohui ʻia, hāʻawi ʻia nā lāʻau e hana e hoʻomaha a wehe i nā kīʻaha koko. ʻO ka poʻe me nā ʻōuli ʻino loa e pono i kahi transplant puʻuwai-lung.

Maikaʻi ka hilinaʻi ʻana o ka mea i luhi ʻia i ka loaʻa ʻana o kahi kūlana olakino ʻē aʻe, a me ka makahiki e ulu ai ke koko kiʻekiʻe i nā akemāmā. Hiki i nā poʻe me kēia ʻano ke ola he 20 a 50 mau makahiki.

Komo pū nā pilikia:

• Kahe ʻana o ka hanu (hemorrhage) i ka lolo
• Hoka puʻuwai Congestive
• Goute
• Maʻi hohola
• Hyperviscosity (sludging o ke koko no ka mea mānoanoa ia me nā huna koko)
• ʻO ka maʻi (abscess) i ka lolo
• Hewa ʻole nā ​​hakuʻala
• Kahe maikaʻi ke koko i ka lolo
• Hahau
• Make make koke

Kāhea i kāu mea hāʻawi inā ulu kāu keiki i nā ʻōuli o ka maʻi ʻo Eisenmenger.

ʻO ke ʻoki ʻana i ka wā hiki ke hoʻoponopono i ka maʻi kīnā o ka puʻuwai hiki ke pale aku iā Eisenmenger Syndrome.

Pākuʻi Eisenmenger; Maʻi Eisenmenger; Ka hopena o Eisenmenger; ʻO Eisenmenger physiology; Hapa puʻuwai Congenital - Eisenmenger; Maʻi maʻi naʻau Cyanotic - Eisenmenger; Puʻuwai kīnā hānau - Eisenmenger

• Eisenmenger syndrome (a paʻakikī paha)

Bernstein D. Nā loina laulā o ka mālama ʻana i nā maʻi puʻuwai congenital. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 461.

ʻO Therrien J, Marelli AJ. ʻO ka maʻi puʻuwai Congenital i nā mākua. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 61.

Webb GD, Smallhorn JF, Therrien J, Redington AN. ʻO ka maʻi puʻuwai Congenital i ke kanaka makua a me ka mea maʻi pediatric. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 75.