Mea Kākau: Clyde Lopez
Lā O Ka Hana: 23 Iulai 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
Hōʻike Donath-Landsteiner - Kino PaʻA
Hōʻike Donath-Landsteiner - Kino PaʻA

ʻO ka ho'āʻo Donath-Landsteiner kahi hōʻike koko e ʻike i nā mea ʻino e pili ana i kahi maʻi maʻamau i kapa ʻia ʻo hemoglobinuria anu paroxysmal. Kūkulu kēia mau mea ʻino a hoʻopau i nā hunaola ʻulaʻula ke hōʻike ʻia ke kino i nā mahana anuanu.

Pono kahi laʻana koko.

ʻAʻole pono kahi hoʻomākaukau kūikawā.

Ke hoʻokomo ʻia ke kui kele e huki i ke koko, manaʻo kekahi poʻe i ka ʻeha kaulike. ʻIke wale kekahi i kahi ʻōniʻu a i ʻole kui. Ma hope, loaʻa paha i kahi kūpikipiki a i ʻole ka ʻūlū iki. Hele koke kēia.

Hana ʻia kēia hōʻike e hōʻoia i kahi kuhi o paroxysmal cold hemoglobinuria.

Manaʻo ʻia ka hoʻāʻo he maʻamau inā ʻaʻohe o nā Donates-Landsteiner antibodies. Kapa ʻia kēia he hopena maikaʻi ʻole.

Hiki ke loli iki nā pae waiwai maʻamau i waena o nā hale hana ʻokoʻa. Hoʻohana kekahi mau labs i nā ana like ʻole a i ʻole nā ​​hoʻāʻo i nā laʻana like ʻole. E kamaʻilio me kāu mea mālama ola e pili ana i ke ʻano o kāu mau hopena hōʻike kikoʻī.

ʻO nā hopena maʻamau ka manaʻo o nā Donath-Landsteiner antibodies. He hōʻailona kēia o paroxysmal cold hemoglobinuria.


ʻAʻohe pilikia iki i ka lawe ʻia ʻana o kou koko. ʻOkoʻa nā aʻa a me nā aʻa i ka nui mai kekahi kanaka a i kekahi ʻē aʻe a mai kekahi ʻaoʻao o ke kino i kekahi. ʻOi aku ka paʻakikī o ka lawe ʻana i ke koko mai kekahi poʻe ma mua o nā poʻe ʻē aʻe.

ʻO nā pilikia ʻē aʻe e pili ana i ke kau ʻana o ke koko he liʻiliʻi, akā hiki ke hoʻopili ʻia:

  • Kahe nui ke koko
  • Pāleʻale a ʻoluʻolu paha
  • Nā punctures he nui e ʻimi i nā uaua
  • Hematoma (kūkulu koko ma lalo o ka ʻili)
  • Maʻiʻaʻai (i iki kamepiula i kēlā me kēia manawa ka ʻili i haki)

Pākuʻi anti-P; ʻO Paroxysmal anuanu hemoglobinuria - Donath-Landsteiner

ʻO Elghetany MT, Schexneider KI, Banki K. Nā maʻi Erythrocytic. I: McPherson RA, Pincus MR, hua. ʻO kā Henry's Clinical Diagnosis a me Management e nā Laboratory Methods. 23rd Ed. St Louis, MO: Elsevier; 2017: chap 32.

ʻO Michel M. Autoimmune a me nā anemias hemolytic intravascular. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 151.


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