Hōʻike mimi Porphyrins

ʻO nā porphyrins he kemika maoli i loko o ke kino e kōkua i ka hana ʻana i nā mea nui i loko o ke kino. ʻO kekahi o kēia he hemoglobin, ka protein i loko o nā hunaola ʻulaʻula e lawe i ka oxygen i loko o ke koko.

Hiki ke ana ʻia nā porphyrins i ka mimi a i ʻole ke koko. Kūkākūkā kēia ʻatikala i ka hoʻāʻo mimi.

Ma hope o kou hāʻawi ʻana i kahi laʻana mimi, ua hoʻāʻo ʻia i ka lab. Kapa ʻia kēia he laʻana mimi huikau.

Inā pono, e noi paha kāu mea mālama ola iā ʻoe e hōʻiliʻili i kou mimi ma ka home ma mua o 24 mau hola. Kapa ʻia kēia he laʻana mimi he 24 mau hola. E haʻi aku kāu mea hāʻawi iā ʻoe pehea e hana ai i kēia. E hāhai pono i nā ʻōkuhi i pololei nā hopena.

E haʻi paha kāu mea lawelawe iā ʻoe e haʻalele no ka lawe manawa ʻana i nā lāʻau e hiki ai ke hoʻololi i nā hopena hōʻike. Pākuʻi ʻia kēia mau mea:

• Nā lāʻau Antibiotics a me nā lāʻau anti-fungal
• Nā lāʻau anti-hopohopo
• Pila pale hānau
• Nā lāʻau diabetes
• Nā lāʻau ʻeha
• Nā lāʻau hoʻomoe

Mai hōʻoki i ka lawe ʻana i nā lāʻau me ka ʻole e kamaʻilio mua i kāu mea hāʻawi.

Hoʻopili kēia hōʻike i ka urination maʻamau wale nō a ʻaʻohe pilikia.

E kauoha kāu mea hāʻawi i kēia hoʻokolohua inā loaʻa nā hōʻailona o ka porphyria a i ʻole nā ​​maʻi ʻē aʻe i hiki ke kumu i nā porphyrins mimi maʻamau.

Hoʻololi nā hopena maʻamau i ka ʻano o ka porphyrin i hoʻāʻo ʻia. Ma ke ʻano laulā, no kahi hōʻike mimi he 24 mau hola o ka nui o nā porphyrins, aia ka pae ma kahi o 20 a 120 µg / L (25 a 144 nmol / L).

Hiki ke loli iki nā pae waiwai maʻamau i waena o nā hale hana ʻokoʻa. Hoʻohana kekahi mau labs i nā ana like ʻole a i ʻole hoʻokolohua i nā hoʻohālikelike like ʻole. E kamaʻilio i kāu mea hāʻawi e pili ana i ke ʻano o kāu mau hopena hōʻike.

Nā hopena kūpono ʻole ma muli o:

• Kanesa maʻi ʻaʻai
• Hepatitis
• Lāʻau make kēpau
• ʻO Porphyria (mau ʻano)

ʻAʻohe pilikia me kēia hōʻike.

Uroporphyrin mimi; Mīkini coproporphyrin; ʻO Porphyria - uroporphyrin

• ʻĀpana mimi wahine
• ʻĀpana mimi kāne
• Hōʻike mimi Porphyrin

ʻO Fuller SJ, Wiley JS. Heme biosynthesis a me kāna mau maʻi: porphyrias a me sideroblastic anemias. I: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 38.

ʻO Riley RS, ʻo McPherson RA. Ninaninau maʻamau o ka mimi. I: McPherson RA, Pincus MR, hua. ʻO kā Henry's Clinical Diagnosis a me Management e nā Laboratory Methods. 23rd Ed. St Louis, MO: Elsevier; 2017: chap 28.