Pectus carinatum

Aia ʻo Pectus carinatum ke puka ka pahu ma luna o ka sternum. Hōʻike pinepine ʻia e like me ka hāʻawi ʻana i kahi kanaka i kahi ʻano manu.
Hiki ke kū hoʻokahi ʻo Pectus carinatum a i ʻole me nā maʻi ʻē aʻe a i ʻole nā syndrome. Kū ke kumu i ka sternum e puka i waho. Aia kekahi kaumaha haiki ma nā ʻaoʻao o ka umauma. Hāʻawi kēia i ka pahu i kahi hiʻohiʻona kūlou e like me ka nūnū.
Hoʻonui ka poʻe me ka pectus carinatum i ka puʻuwai maʻamau a me nā māmā. Eia nō naʻe, pale paha ka deformity i kēia mau mea mai ka hana ʻana e like me ka hiki iā lākou. Aia kekahi mau hōʻike e hiki i ka pectus carinatum ke pale aku i ka ninini piha ʻana o ka ea mai nā ake māmā i nā keiki. Heʻuʻuku paha ka ikaika o kēia poʻe ʻōpio, ʻoiai inā ʻaʻole lākou e ʻike.
Hiki i nā pectus deformities ke hopena i ka kiʻi ponoʻī o kahi keiki. Noho hauʻoli kekahi mau keiki me pectus carinatum. No nā poʻe ʻē aʻe, hiki i ke kinona o ka umauma ke hōʻino i ko lākou ʻano ponoʻī a me ka hilinaʻi iā ia iho. Hoʻopilikia paha kēia mau manaʻo i ka pili ʻana i nā poʻe ʻē aʻe.
Nā kumu e komo pū paha:
- Congenital pectus carinatum (aia ma ka hānau ʻana)
- Trisomy 18
- ʻO Trisomy 21
- Homocystinuria
- Maʻi ʻo Marfan
- Maʻi Morquio
- ʻO ka maʻi lentigines maha
- Osteogenesis sempurnaa
I nā manawa he nui ʻaʻole ʻike ʻia ke kumu.
ʻAʻole pono kahi mālama home kūpono no kēia ʻano.
Kāhea i kāu mea mālama ola inā ʻike ʻoe i ka umauma o kāu keiki me he mea ʻole lā ke ʻano.
E hana ka mea hāʻawi i kahi hoʻokolohua kino a nīnau i nā nīnau e pili ana i ka mōʻaukala o ke keiki a me nā hōʻailona. Hiki i nā nīnau ke komo pū me:
- I ka manawa hea ʻoe i ʻike mua ai i kēia? Aia i ka wā hānau, a i ulu paha i ka ulu ʻana o ke keiki?
- Ke hele nei a maikaʻi, ʻino, a noho like paha?
- He aha nā hōʻailona ʻē aʻe e kū nei?
ʻO nā hoʻāʻo e hana ʻia ana paha:
- ʻO ka hoʻāʻo ʻana i ka hana Lung e ana i ke ʻano o ka hana ʻana o ka puʻuwai a me nā māmā
- Nā hoʻokolohua lab e like me ka chromosome haʻawina, nā enzyme assays, x-ray, a i ʻole nā metabolic haʻawina
Hoʻohana ʻia kahi paʻa e mālama ai i nā keiki a me nā ʻōpio ʻōpio. Hana ʻia ke ʻoki kino i kekahi manawa. Ua loaʻa i kekahi poʻe ka hoʻomaikaʻi hoʻoikaika kino a me ka maikaʻi o ka hana māmā ma hope o ke kahakaha ʻana.
Pigeon umauma; Umauma Pigeon
Lipine
Puku umauma (nūnū umauma)
ʻO Boas SR. Nā maʻi skeletal e hoʻoliʻiliʻi ana i ka hana pulmonary. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 445.
Graham JM, Sanchez-Lara PA. ʻO Pectus excavatum a me pectus carinatum. I: Graham JM, Sanchez-Lara PA, hua. Nā Manaʻo Hoʻomaopopo a Smith o ka Hoʻololi Kānaka. ʻEhā ed. Piladelapia, PA: Elsevier; 2016: chap 19.
Kelly RE, Martinez-Ferro M. Nā hemahema o ka paia. I: Holcomb GW, Murphy JP, St. Peter SD eds. ʻO Surgery Pediatricʻo Ashcraft. ʻEpekema 7 Piladelapia, PA: Elsevier; 2020: chap 20.