Mea Kākau: Janice Evans
Lā O Ka Hana: 3 Iulai 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
Pectus Carinatum
Wikiō: Pectus Carinatum

Aia ʻo Pectus carinatum ke puka ka pahu ma luna o ka sternum. Hōʻike pinepine ʻia e like me ka hāʻawi ʻana i kahi kanaka i kahi ʻano manu.

Hiki ke kū hoʻokahi ʻo Pectus carinatum a i ʻole me nā maʻi ʻē aʻe a i ʻole nā ​​syndrome. Kū ke kumu i ka sternum e puka i waho. Aia kekahi kaumaha haiki ma nā ʻaoʻao o ka umauma. Hāʻawi kēia i ka pahu i kahi hiʻohiʻona kūlou e like me ka nūnū.

Hoʻonui ka poʻe me ka pectus carinatum i ka puʻuwai maʻamau a me nā māmā. Eia nō naʻe, pale paha ka deformity i kēia mau mea mai ka hana ʻana e like me ka hiki iā lākou. Aia kekahi mau hōʻike e hiki i ka pectus carinatum ke pale aku i ka ninini piha ʻana o ka ea mai nā ake māmā i nā keiki. Heʻuʻuku paha ka ikaika o kēia poʻe ʻōpio, ʻoiai inā ʻaʻole lākou e ʻike.

Hiki i nā pectus deformities ke hopena i ka kiʻi ponoʻī o kahi keiki. Noho hauʻoli kekahi mau keiki me pectus carinatum. No nā poʻe ʻē aʻe, hiki i ke kinona o ka umauma ke hōʻino i ko lākou ʻano ponoʻī a me ka hilinaʻi iā ia iho. Hoʻopilikia paha kēia mau manaʻo i ka pili ʻana i nā poʻe ʻē aʻe.


Nā kumu e komo pū paha:

  • Congenital pectus carinatum (aia ma ka hānau ʻana)
  • Trisomy 18
  • ʻO Trisomy 21
  • Homocystinuria
  • Maʻi ʻo Marfan
  • Maʻi Morquio
  • ʻO ka maʻi lentigines maha
  • Osteogenesis sempurnaa

I nā manawa he nui ʻaʻole ʻike ʻia ke kumu.

ʻAʻole pono kahi mālama home kūpono no kēia ʻano.

Kāhea i kāu mea mālama ola inā ʻike ʻoe i ka umauma o kāu keiki me he mea ʻole lā ke ʻano.

E hana ka mea hāʻawi i kahi hoʻokolohua kino a nīnau i nā nīnau e pili ana i ka mōʻaukala o ke keiki a me nā hōʻailona. Hiki i nā nīnau ke komo pū me:

  • I ka manawa hea ʻoe i ʻike mua ai i kēia? Aia i ka wā hānau, a i ulu paha i ka ulu ʻana o ke keiki?
  • Ke hele nei a maikaʻi, ʻino, a noho like paha?
  • He aha nā hōʻailona ʻē aʻe e kū nei?

ʻO nā hoʻāʻo e hana ʻia ana paha:

  • ʻO ka hoʻāʻo ʻana i ka hana Lung e ana i ke ʻano o ka hana ʻana o ka puʻuwai a me nā māmā
  • Nā hoʻokolohua lab e like me ka chromosome haʻawina, nā enzyme assays, x-ray, a i ʻole nā ​​metabolic haʻawina

Hoʻohana ʻia kahi paʻa e mālama ai i nā keiki a me nā ʻōpio ʻōpio. Hana ʻia ke ʻoki kino i kekahi manawa. Ua loaʻa i kekahi poʻe ka hoʻomaikaʻi hoʻoikaika kino a me ka maikaʻi o ka hana māmā ma hope o ke kahakaha ʻana.


Pigeon umauma; Umauma Pigeon

  • Lipine
  • Puku umauma (nūnū umauma)

ʻO Boas SR. Nā maʻi skeletal e hoʻoliʻiliʻi ana i ka hana pulmonary. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 445.

Graham JM, Sanchez-Lara PA. ʻO Pectus excavatum a me pectus carinatum. I: Graham JM, Sanchez-Lara PA, hua. Nā Manaʻo Hoʻomaopopo a Smith o ka Hoʻololi Kānaka. ʻEhā ed. Piladelapia, PA: Elsevier; 2016: chap 19.

Kelly RE, Martinez-Ferro M. Nā hemahema o ka paia. I: Holcomb GW, Murphy JP, St. Peter SD eds. ʻO Surgery Pediatricʻo Ashcraft. ʻEpekema 7 Piladelapia, PA: Elsevier; 2020: chap 20.


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