Mea Kākau: William Ramirez
Lā O Ka Hana: 20 Kepakemapa 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Wikiō: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias he liʻiliʻi, hoʻonui ʻia nā kīʻaha koko ma ka ʻili. ʻAʻole hōʻeha lākou, akā pili pū paha me nā maʻi he nui.

Hiki i nā Telangiectasias ke ulu i nā wahi āpau o ke kino. Akā ʻike maʻalahi ʻia lākou ma ka ʻili, nā membrane mucous, a me nā keʻokeʻo o nā maka. ʻO ka maʻamau, ʻaʻole lākou e kumu i nā ʻōuli. Ua kahe kekahi mau telangiectasias a hana i nā pilikia nui. Hiki i nā Telangiectasias ke hana i ka lolo a i ʻole nā ​​ʻōpū a hana i nā pilikia nui mai ke kahe ʻana.

Nā kumu e komo pū paha:

  • Rosacea (ʻili pilikia e hoʻohuli i ka maka i ʻulaʻula)
  • ʻElemakule
  • Pilikia me nā gen
  • Hapai keiki
  • Hōʻike lā
  • ʻO nā veins varicose
  • Hoʻohana nui ʻia i nā kalima steroid
  • Trauma i ka wahi

Nā maʻi e pili pū ana me kēia ʻano:

  • Ataxia-telangiectasia (maʻi e hoʻopili i ka ʻili, ke kaulike a me ka hoʻohui ʻana, a me nā wahi ʻē aʻe o ke kino)
  • Bloom Syndrome (hoʻoilina maʻi e kumu i ke kino pōkole, ʻike ka ʻili i nā kukuna ultraviolet o ka lā, a me ka ʻulaʻula o ka maka)
  • ʻO Cutis marmorata telangiectatica congenita (ka maʻi ʻili e hoʻopiʻi ana i nā ʻulaʻula)
  • ʻO ka telangectasia hemorrhagic heereditary (Osler-Weber-Rendu syndrome)
  • ʻO Klippel-Trenaunay-Weber Syndrome (maʻi e kumu ai i ka port-wine stain, varicose veins, a me nā pilikia palupalu)
  • ʻO Nevus flammeus e like me ka stain waina-awa
  • ʻO Rosacea (ke ʻano o ka ʻili e ʻula ai ka maka)
  • ʻO Sturge-Weber maʻi (maʻi e pili ana i ka port-waina stain a me nā ʻōnaehana ʻōnaehana pilikia)
  • Xeroderma pigmentosa (maʻi kahi e ʻili loa ai ka ʻili a me nā mea i uhi i ka maka i ka malamalama ultraviolet)
  • Lupus (maʻi ʻōnaehana maʻi)
  • CREST Syndrome (kahi ʻano o scleroderma e pili ana i ke kūkulu ʻia ʻana o nā ʻili e like me ka maka i ka ʻili a me nā wahi ʻē aʻe o ke kino a hōʻino hoʻi i nā hunaola e kū ana i nā paia o nā aʻa liʻiliʻi)

Kāhea i kāu mea mālama ola inā ʻike ʻoe i nā moku hoʻonui i ka ʻili, nā membrane mucous, a i ʻole nā ​​maka.


E hana ka mea hāʻawi i kahi hoʻokolohua kino a nīnau e pili ana i kāu mau hōʻailona, ​​e like me:

  • Aia ma hea nā kīʻaha koko?
  • Māmā wale ke koko a me ke kumu ʻole?
  • He aha nā hōʻailona ʻē aʻe e kū nei?

Pono paha nā hoʻokolohua e hōʻoia a kāpae paha i kahi ʻano olakino. E komo pū paha nā hoʻāʻo:

  • Nā hoʻāʻo koko
  • Nānā CT
  • Haʻawina hana ate
  • Nānā MRI
  • Nā kukuna X

ʻO Sclerotherapy ka lapaʻau no nā telangiectasias ma nā wāwae. I kēia kaʻina hana, hoʻopili ʻia kahi wai paʻakai (paʻakai) a i ʻole nā ​​kemika ʻē aʻe i loko o nā veins spider ma nā wāwae. Hoʻohana pinepine ʻia ka lapaʻau laser e mālama i nā telangiectasias o ka maka.

ʻO ectasias Vascular; Punawelewele angioma

  • Angioma serpiginosum
  • Telangiectasia - nā wāwae
  • Telangiectasias - lima luna

Kelly R, Baker C. Nā maʻi maʻi ʻē aʻe. I: Bolognia JL, Schaffer JV, Cerroni L, eds. Dermatology. ʻEhā ed. Piladelapia, PA: Elsevier; 2018: chap 106.


Patterson JW. ʻO nā kūpuna vascular. I: Patterson JW, hoʻoponopono. ʻO Weedon's Skin Pathology. ʻEhā ed. Piladelapia, PA: Elsevier Churchill Livingstone; 2016: chap 38.

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