Subacute sclerosing panencephalitis

ʻO Subacute sclerosing panencephalitis (SSPE) kahi holomua, hoʻopau ʻole, a me ka maʻi lolo e pili ana i ka maʻi measles (rubeola).

Hoʻolālā ka maʻi i nā makahiki he nui ma hope o ka maʻi maʻi tigā.

ʻO ka maʻamau, ʻaʻole ka maʻi maʻi ʻo ka maʻi ʻula e hoʻopōʻino i ka lolo. Eia nō naʻe, hiki i kahi pane pale pale kūlohelohe i ka maʻi ʻula a i ʻole, malia paha, hiki i kekahi ʻano mutant o ka maʻi ke hana i nā maʻi nui a me ka make. ʻO kēia pane e alakaʻi ai i ka mumū o ka lolo (ka pehu a me ka huhū) i mau paha i mau makahiki.

Ua hōʻike ʻia ʻo SSPE ma nā wahi āpau o ka honua, akā ma nā ʻāina komohana he maʻi maʻamau ia.

ʻIke liʻiliʻi loa nā hihia i ʻike ʻia ma ʻAmelika Hui Pū ʻIa mai ka wā i hoʻomaka ai ka papahana hoʻōla lāʻau ʻōiwi āpau. Kū pinepine ʻo SSPE i kekahi mau makahiki ma hope o ka loaʻa ʻana o ka maʻi ʻula i ke kanaka, ʻoiai ua ola pono ke kanaka mai ka maʻi. Hoʻopilikia pinepine ʻia nā kāne ma mua o nā wahine. Kū ka maʻi i nā keiki a me nā ʻōpio.

Hana ʻia nā ʻōuli o SSPE i nā hanana holo ʻehā. Me kēlā me kēia pae, ʻoi aku ka maikaʻi o nā ʻōuli ma mua o ke kahua ma mua.

• Kahua I: Aia paha he hoʻololi pilikino, hoʻololi o ke ʻano, a kaumaha paha. ʻO ka fiva a me ka ʻeha poʻo. Hiki i kēia pae ke 6 mau mahina.
• ʻOihana II: Aia paha he mau pilikia neʻe ʻole e kaohi ʻia e like me ka jerking a me nā spasms muscle. ʻO nā ʻōuli ʻē aʻe e kū i kēia pae ka nalowale o ka hihiʻo, dementia, a me ka hopu ʻana.
• Kahua III: Hoʻololi ʻia nā neʻe ʻana i ka neʻe ʻana e ka ʻoki ʻana (wili) ʻana a me ka paʻakikī. Hiki ke make i nā pilikia.
• ʻOihana IV: Nā wahi o ka lolo e kaohi ana i ka hanu ʻana, ka helu o ka puʻuwai, a me ke kaomi koko i hōʻino ʻia. ʻO kēia ke alakaʻi i ke koma a laila ka make.

Aia paha he mōʻaukala o ka maʻi ʻula no kahi keiki unvaccinated. Hōʻike kahi loiloi kino:

• Poino i ke aʻalolo optic, ke kuleana o ka ʻike maka
• Poino i ka retina, ka ʻāpana o ka maka i loaʻa ka mālamalama
• ʻ .wili mākala
• Hana maikaʻi ʻole ma nā hoʻokolohua hoʻohuihui motor (neʻe)

E hana ʻia paha kēia mau hoʻāʻo:

• Electroencephalogram (EEG)
• Koʻo MRI
• ʻO ka titer antibody serum e nānā i nā hōʻailona o ka maʻi o ka maʻi ʻula mua
• Piula ʻōiwi

ʻAʻohe mea ola no SSPE. Hoʻopaʻa pinepine ʻia ka mālama ʻana i ka kaohi ʻana i nā ʻōuli. Hiki ke hoʻāʻo ʻia kekahi mau lāʻau antiviral a hoʻonui i ka ʻōnaehana pale e hoʻolohi i ka holomua o ka maʻi.

Hiki i nā kumuwaiwai aʻe ke hāʻawi i ka ʻike hou aku ma SSPE:

• National Institute of Neurological Disorder a me ka hahau - www.ninds.nih.gov/Disorder/All-Disorders/Subacute-Sclerosing-Panencephalitis-Information-Page
• National Organization for Rare Disorder - rarediseases.org/rare-diseases/subacute-sclerosing-panencephalitis/

He mea make ʻo SSPE mau. Make ka poʻe me kēia maʻi i 1 a 3 mau makahiki ma hope o ka hōʻailona. E ola lōʻihi paha kekahi poʻe.

Kāhea i kāu kahu mālama ola inā ʻaʻole i hoʻokō kāu keiki i kā lākou lāʻau āpau. Hoʻokomo ʻia ka lāʻau koʻokoʻo no ka maʻi ʻula.

ʻO ka pale ʻana i ka maʻi ʻula ka mea ʻike nui ʻia e pale ai no SSPE. Ua maikaʻi ka lāʻau lapaʻau o ka maʻi ʻula no ka hoʻemi ʻana i nā helu o nā keiki i hoʻopilikia ʻia.

Pono e hana i ka pale ʻana i ka lapalapa e like me ka ʻōlelo a ka American Academy of Pediatrics a me nā kikowaena no ka papa kuhikuhi no ka maʻi.

SSPE; Subacute sclerosing leukoencephalitis; Dawson encephalitis; Nā ana - SSPE; Rubeola - SSPE

ʻO Gershon AA. ʻO ka maʻi hoʻomaʻi maʻi (rubeola). I: Bennett JE, Dolin R, Blaser MJ, hua pā. ʻO Mandell, Douglas, a me Bennett's Principle a me ka hoʻomaʻamaʻa ʻana i nā maʻi kūpilikiʻi. 9th ed. Piladelapia, PA: Elsevier; 2020: chap 160.

ʻO Mason WH, ʻo Gans HA. ʻLeskala. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 273.