ʻO Sydenham chorea
![Boy with Sydenham’s Chorea](https://i.ytimg.com/vi/wTCnbga3sqg/hqdefault.jpg)
ʻO Sydenham chorea kahi maʻi neʻe i kū ma hope o ka maʻi ʻana me kekahi mau bacteria i kapa ʻia ʻo ka hui A streptococcus.
Hoʻokumu ʻia ʻo Sydenham chorea e kahi maʻi me nā bacteria i kapa ʻia ʻo ka hui A streptococcus. ʻO kēia ka maʻi bacteria e kumu ai i ka fiva rumatika (RF) a me ka ʻāʻī strep. Hiki i nā hui bacteria A streptococcus ke hana me kahi ʻāpana o ka lolo i kapa ʻia ʻo basal ganglia e hana i kēia maʻi. ʻO ka baslia ganglia kahi hoʻonohonoho o nā hale i hohonu i ka lolo. Kōkua lākou i ka kaohi i ke neʻe, ke kūlana, a me ka ʻōlelo.
ʻO Sydenham chorea kahi hōʻailona nui o RF koʻikoʻi. Ua loaʻa paha i kēia kanaka ka maʻi i kēia manawa. ʻO Sydenham chorea wale nō ka hōʻailona o RF i kekahi poʻe.
Hana pinepine ʻo Sydenham chorea i nā kaikamahine ma mua o ka wā ʻōpio, akā ʻike ʻia paha i nā keikikāne.
ʻO ka hana nui a Sydenham chorea me ka neʻe ʻole a me ka neʻe ʻole ʻana o nā lima, nā lima, ka poʻohiwi, ke alo, nā wāwae, a me ke kumu. Ke nānā nei kēia mau neʻe e like me twitches, a nalo i ka wā hiamoe. Hiki i nā ʻōuli ʻē aʻe ke:
- Hoʻololi i ka kākau lima ʻana
- Ka lilo o ke kaʻa moto maikaʻi, keu hoʻi o nā manamana lima a me nā lima
- Ka nalowale ʻana o ka naʻau, me ka uē a me ka ʻakaʻaka ʻana
Aia paha nā ʻōuli o RF. Pākuʻi paha kēia i ke kuni kiʻekiʻe, ka pilikia o ka puʻuwai, ka ʻeha pū ʻana a i ʻole ka pehu ʻana, nā puʻupuʻu o ka ʻili a me nā huehue o ka ʻili, a me nā ihu ihu.
E hana ka mea mālama ola i kahi hoʻokolohua kino. E nīnau ʻia nā nīnau kikoʻī e pili ana i nā ʻōuli.
Inā manaʻo ʻia kahi maʻi streptococcus, e hana ʻia nā hōʻike e hōʻoia i ka maʻi. Pākuʻi ʻia kēia mau mea:
- ʻŪhā puʻupuʻu
- Hōʻike koko Anti-DNAse B
- Hōʻike koko Antistreptolysin O (ASO)
Hiki i nā hoʻokolohua hou aʻe ke:
- Nā ho'āʻo koko e like me ESR, CBC
- MRI a i ʻole CT scan o ka lolo
Hoʻohana ʻia nā lāʻau antibiotic e pepehi i nā koʻohune streptococcus. Kauoha paha ka mea hāʻawi i nā lāʻau antibiotic e pale i nā maʻi RF e hiki mai ana. Kapa ʻia kēia he antibiotic preventive, a he antibiotic prophylaxis.
Pono e mālama ʻia ka neʻe ʻana a i ʻole nā ʻōuli o ka naʻau me nā lāʻau.
Hoʻomaʻemaʻe ʻo Sydenham chorea i kekahi mau mahina. I nā hihia maʻamau, hoʻomaka paha kahi ʻano ʻokoʻa o ka chorea Sydenham ma hope o ke ola.
ʻAʻohe pilikia e manaʻo ʻia.
Kāhea i kāu mea hāʻawi inā ulu aʻe kāu keiki i ka neʻe ʻole a i ʻole ka neʻe ʻana o ka neʻe, keu hoʻi inā he ʻeha ka ʻāʻī o ke keiki.
E nānā pono i nā hoʻopiʻi a nā keiki no nā ʻāʻī ʻeha a loaʻa i ka lāʻau lapaʻau mua e pale ai i ka RF nui. Inā loaʻa kahi moʻolelo ʻohana ikaika o RF, e makaʻala loa, no ka mea e ulu ana paha kāu mau keiki i kēia maʻi.
Hula ʻo St. Vitus; Chorea ʻōpio; Chorea rumatika; Rheumatic fever - Sydenham chorea; Strep puʻu - Sydenham chorea; Streptococcal - Sydenham chorea; Streptococcus - Sydenham chorea
ʻO Jankovic J. Parkinson maʻi a me nā ʻano neʻe ʻē aʻe. I: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, eds. ʻO Bradley's Neurology i ka hana lapaʻau. ʻEpekema 7 Piladelapia, PA: Elsevier; 2016: chap 96.
Okun MS, Lang AE. Nā pilikia neʻe ʻē aʻe. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 382.
Shulman ST, Jaggi P. Nonsuppurative poststreptococcal sequelae: rumatika fever a me glomerulonephritis. I: Bennett JE, Dolin R, Blaser MJ, hua pā. ʻO Mandell, Douglas, a me Bennett's Principle a me ka hoʻomaʻamaʻa ʻana i nā maʻi kūpilikiʻi. 9th ed. Piladelapia, PA: Elsevier; 2020: chap 198.