ʻO ka maʻi ʻōpū ʻo Prune

ʻO ka maʻi ʻōpū ʻo Prune kahi hui o nā hānau hānau maʻamau e pili ana i kēia mau pilikia nui ʻekolu.

• Hoʻonui maikaʻi ʻole o nā mākala o ka ʻōpū, e wīwī ai ka ʻili o ka ʻōpū e like me ka prune
• Hōkū hōʻike ʻole ʻia
• Nā pilikia o ka mimi

ʻAʻole ʻike ʻia nā kumu kikoʻī o ka prune ʻōpū maʻi. Hoʻopili ke ʻano i nā keikikāne.

ʻOiai i loko o ka ʻōpū, pehu ka ʻōpū o ka pēpē e ulu ana me ka wai. ʻO ka manawa pinepine, he pilikia ke kumu i ka maʻi urinary. Nalo ka wai ma hope o ka hānau ʻana, a hiki i ka ʻōpū kukū e like me ka prune. ʻIke ʻia kēia hiʻohiʻona ma muli o ka nele o nā mākala ʻōpū.

Hiki i nāʻiʻo ʻōpū palupalu ke kumu:

• Konipōpō
• Hoopanee i ka noho a me ka hele wāwae ʻana
• Nā paʻakikī paʻakikī

Hiki i nā pilikia o ke urinary ke pilikia i ka mimiki.

ʻO ka wahine hāpai i ka pēpē i loaʻa i ka prune ʻōpū maʻi ʻaʻole lawa paha ka wai amniotic (ka wai e hoʻopuni ana i ka fetus). Hiki i kēia pēpē ke loaʻa i nā pēpē pilikia mai ka kaomi ʻana i ka ʻōpū.

Hana ʻia kahi ultrasound i ka wā o ka hāpai ʻana e hōʻike i ka pēpē i ka bladen bladder a i ʻole hoʻonui ʻia ka hakuʻala.

I kekahi mau hihia, hiki i kahi ultrasound hāpai ke kōkua pū i ka hoʻoholo inā loaʻa i ka pēpē:

• Nā pilikia puʻuwai
• Iwi maʻamau a i ʻole nā ​​mākala
• Nā pilikia ʻōpū a me nā ʻōpū
• Nā māmā i hoʻomohala ʻole ʻia

E hana ʻia paha kēia mau hoʻokolohua ma luna o ka pēpē ma hope o ka hānau ʻana e hōʻike i ke ʻano o ke ʻano.

• Nā hoʻāʻo koko
• ʻO ka pyelogram Intravenous (IVP)
• Kukuna ultrasound
• Voiding cystourethrogram (VCUG)
• X-ray
• CT scan
  

Paipai ʻia ke ʻoki mua e hoʻoponopono i nā mākala palupalu nāwaliwali, nā pilikia o ka urinary tract, a me nā testicle undescended.

Hāʻawi ʻia ka pēpē i nā antibiotic e mālama a kōkua ai i ka pale ʻana i nā maʻi maʻi urinary.

Hiki i nā kumuwaiwai aʻe ke hāʻawi i ka ʻike hou aku e pili ana i ka maʻi ʻōpū prune:

• Pūnaewele ʻo Prune Belly Syndrome - prunebelly.org
• National Organization for Rare Disorder - rarediseases.org/rare-diseases/prune-belly-syndrome

ʻO Prune ʻōpū maʻi kahi pilikia koʻikoʻi a hoʻoweliweli pinepine i ke ola.

He nui nā pēpē me kēia ʻano hanau hānau a make paha i loko o nā pule mua o ke ola. ʻO ke kumu o ka make mai nā pilikia nui o ka hū a me nā puʻupaʻa, a mai ka hui pū ʻana o nā pilikia hānau.

Ola kekahi mau keiki hānau hou a hiki ke hoʻomohala maʻamau. Hoʻomau ka poʻe ʻē aʻe i nā pilikia olakino a me nā hoʻomohala he nui.

Pili nā pilikia ma nā pilikia pili. ʻO nā mea maʻamau ʻo:

• Konipōpō
• Nā iwi deformities (clubfoot, dislocated hip, nalowale nā ​​lālā, ka manamana, a me ka manamanalima, ka umauma funnel)
• ʻO ka maʻi o ka maʻi urinary (pono paha i ka dialysis a me kahi transplant kidney)

Hiki i nā testicle ʻole ke alakaʻi i ka infertility a i ʻole ke kanesa.

Hoʻomaopopo pinepine ʻia ka maʻi ʻōpū ʻo Prune ma mua o ka hānau ʻana a i ka wā e hānau ʻia ai ka pēpē.

Inā loaʻa iā ʻoe kahi keiki me ka maʻi ʻōpū prune ʻōpū, e kāhea i kāu mea mālama ola ma ka hōʻailona mua o kahi maʻi urinary tract a i ʻole nā ​​hōʻailona urinary ʻē aʻe.

Inā hōʻike kahi ultrasound hāpai keiki i kāu pēpē i ka bladen bladder a i hoʻonui ʻia paha nā puʻupaʻa, e kamaʻilio me kahi loea i ka hāpai kiʻekiʻe a me ka perinatology.

ʻAʻohe ala i ʻike ʻia e pale ai i kēia ʻano. Inā ʻike ʻia ka pēpē me kahi ālai maʻi urinary ma mua o ka hānau ʻana, i nā manawa kakaikahi, hiki i ke ʻoki ʻana i ka wā o ka hāpai ke pale aku i ka pilikia mai ka holomua ʻana i ka maʻi o ka ʻōpū.

Eagle-Barrett maʻi maʻi; ʻO Triad Syndrome

ʻO Caldamone AA, Denes FT. ʻO Prune-ʻōpū maʻi maʻi. I: Wein AJ, Kavoussi LR, Partin AW, Peters CA, eds. Campbell-Walsh Urology. 11th hua. Piladelapia, PA: Elsevier; 2016: chap 140.

ʻO Elder JS. ʻO ka ālai ʻana o ka maʻi urinary. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 555.

ʻO Merguerian PA, Rowe CK. ʻO nā hanana kūpono ʻole o ka ʻōnaehana genitourinary. I: Gleason CA, Juul SE, eds. Nā maʻi o Avery o ke keiki hānau. 10 o ka lā. Piladelapia, PA: Elsevier; 2018: chap 88.