Truncus arteriosus

ʻO Truncus arteriosus kahi ʻano maʻi maʻi puʻuwai kahi e puka ai kahi kīʻaha koko hoʻokahi (truncus arteriosus) mai ka ventricle ʻākau a hema, ma kahi o nā moku 2 maʻamau (pulmonary artery and aorta). Aia ia i ka wā hānau (maʻi puʻuwai congenital).

Aia kekahi mau ʻano truncus arteriosus.

I ka holo maʻamau, puka ka aʻa o ka pulmonary mai ka ventricle ʻākau a puka ka aorta mai ka ventricle hema, ka mea kaʻawale kekahi i kekahi.

Me nā truncus arteriosus, puka mai kahi aʻa hoʻokahi mai nā ventricle. Aia kekahi pinepine i puka nui ma waena o nā ventricle 2 (hemahema septal ventricular). A ʻo kahi hopena, hui pū ka uliuli (me ka ʻole o oxygen) a me ka ʻulaʻula (waiwai-oxygen).

Hele kekahi o kēia koko hui i nā akemāmā, a hele kekahi i ke koena o ke kino. ʻO ka pinepine, ʻoi aku ka nui o ke koko ma mua o ka hopena e hele i nā ake māmā.

Inā mālama ʻole ʻia kēia ʻano, loaʻa ʻelua mau pilikia:

• ʻO ka nui o ke kahe o ke koko i loko o nā akemāmi e hoʻoulu ai i ka wai keu a puni iā ​​lākou. He mea paʻakikī kēia e hanu.
• Inā haʻalele ʻole ʻia a ʻoi aku ma mua o ke kahe o ke koko e kahe ana i nā akemāmā no ka manawa lōʻihi, lilo nā kīʻaha koko i nā akemāmā i mea mau pōʻino. I ka hala ʻana o ka manawa, lilo i mea paʻakikī loa ka naʻau e hoʻoikaika i ke koko iā lākou. Kāhea ʻia kēia ʻo ka pulmonary hypertension, hiki ke hoʻoweliweli i ke ola.

ʻO nā hōʻailona me:

• ʻO kaʻili Bluish (cyanosis)
• Hoʻolohi ʻia ka ulu ʻana a i ʻole ulu holomua
• Ka luhi
• Lethargy
• ʻAi hānai maikaʻi ʻole
• Ka hanu wikiwiki ʻana (tachypnea)
• Ka hanu o ka hanu (dyspnea)
• Ke hoʻonui nei i nā ʻōlelo aʻoaʻo a ka manamana lima (clubbing)

Lohe pinepine ʻia ka ʻōhumu ke hoʻolohe i ka puʻuwai me kahi stethoscope.

Loaʻa i nā hoʻāʻo:

• ECG
• ʻEchocardiogram
• Pākuʻi x-ray
• ʻO ka catheterization Cardiac
• MRI a i ʻole CT scan o ka puʻuwai

Pono ke ʻoki kino e mālama i kēia ʻano. Hana ke ʻoki i 2 aʻa ʻokoʻa.

I ka hapanui o nā hihia, mālama ʻia ka ipu truncal ma ke ʻano he aorta hou. Hoʻokumu ʻia kahi aʻa pulmonary hou me ka hoʻohana ʻana i ka iʻa mai kahi kumu ʻē aʻe a i ʻole ka hoʻohana ʻana i kahi Tube hana kanaka. Humuhumu ʻia nā aʻa pulmonary lālā i kēia aʻa hou. Pani ʻia ka puka ma waena o nā ventricle.

Hāʻawi pinepine i ka hoʻoponopono hou i nā hopena maikaʻi. Pono paha kahi hana ʻē aʻe i ka ulu ʻana o ke keiki, no ka mea, ʻaʻole e ulu ka pulmonary artery e hoʻohana ana i ka iʻa mai kahi kumu ʻē aʻe me ke keiki.

ʻO nā hihia i mālama ʻole ʻia o truncus arteriosus ka hopena i ka make, pinepine i ka makahiki mua o ke ola.

Komo pū nā pilikia:

• Hewa puʻuwai
• ʻO ke koko kiʻekiʻe i loko o nā māmā (hypertension pulmonary)

Kāhea i kāu kahu mālama ola inā kāu pēpē a keiki paha:

• ʻIke lethargic
• ʻIke i ka luhi nui a i ʻole ka liʻiliʻi o ka hanu
• ʻAi maikaʻi ʻole
• ʻAʻole e ulu a ulu ana paha i ka maʻamau

Inā ʻuli polū ka ʻili, nā lehelehe, a me nā moena kui a inā paha he pōkole ka hanu o ke keiki, lawe i ke keiki i ka lumi pilikia a i ʻole e nānā koke ke keiki.

ʻAʻohe pale e ʻike ʻia. Hiki i ka mālama mua ʻana ke pale pinepine i nā pilikia koʻikoʻi.

ʻO Truncus

• ʻOki puʻuwai Pediatric - hoʻokuʻu

• Puʻuwai - ʻāpana ma waena o ka waena
• Truncus arteriosus

Fraser CD, Kane LC. Maʻi maʻi ʻōpū. I: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. ʻO Sabiston Textbook of Surgery: Ke kumu kumu olaola o ka hana ʻoki ʻana o kēia ao. 20 ouk. Piladelapia, PA: Elsevier; 2017: chap 58.

Webb GD, Smallhorn JF, Therrien J, Redington AN. ʻO ka maʻi puʻuwai Congenital i ke kanaka makua a me ka mea maʻi pediatric. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 75.