ʻO ka palsy supranuclear holomua

ʻO ka palsy holomua supranuclear holomua (PSP) kahi maʻi neʻe e kū mai ka hōʻino ʻana i kekahi mau pūnana nerve i ka lolo.

ʻO PSP kahi ʻano e hoʻokumu i nā ʻōuli e like me ka maʻi Parkinson.

Pili ia i ka hōʻino ʻana i nā hunaola he nui o ka lolo. Hoʻopili ʻia nā wahi he nui, e like me ka ʻāpana o ka lolo i kahi o nā hunaola e kaohi ana i ka neʻe ʻana o ka maka. Hoʻopili pū ʻia kahi o ka lolo e kaohi ana i ke kūpaʻa ke hele ʻoe. Hoʻopili pū ʻia nā lobes mua o ka lolo, e alakaʻi ana i nā loli pilikino.

ʻAʻole ʻike ʻia ke kumu o ka hōʻino ʻana i nā hunaola o ka lolo. Hoʻonui ʻo PSP i ka hala ʻana o ka manawa.

Loaʻa nā poʻe me PSP i nā waihona lolo e like me nā mea i loaʻa i ka poʻe me ka maʻi Alzheimer. Loaʻa ka nalo o nā kiko i ka hapa nui o nā wahi o ka lolo a ma kekahi mau wahi o ka iwi kuamoʻo.

ʻIke pinepine ʻia kēia maʻi i nā poʻe ma mua o 60 mau makahiki, a ʻoi aku ka maʻamau o nā kāne.

Pākuʻi ʻia paha nā ʻōuli i kekahi o kēia mau mea:

• Lilo o ke kaulike, hāʻule hou
• Ke hele nei i mua ke neʻe, a me ka hele wāwae wikiwiki
• Pākuʻi i nā mea a kanaka paha
• Hoʻololi i nā hiʻohiʻona o ka helehelena
• Helehelena hohonu
• Nā pilikia o ka maka a me ka hihiʻo e like me nā haumāna ʻokoʻa ka nui, ka paʻakikī e neʻe i nā maka (supranuclear ophthalmoplegia), ka ʻole o ka kaohi o nā maka, nā pilikia e wehe ka maka.
• Pilikia i ka ale ʻana
• ʻO nā haʻalulu, ka iwi ā, a i ʻole nā ​​helehelena
• Dementia akahai
• Hoʻololi ka pilikino
• Holo mālie a paʻakikī paha
• Nā pilikia ʻōlelo, e like me ka leo o ka leo haʻahaʻa, ʻaʻole hiki ke ʻōlelo i nā huaʻōlelo me ka maopopo, ʻōlelo lohi
• ʻO ka paʻakikī a me ka neʻe o ka ʻāʻī, waena o ke kino, nā lima, a me nā wāwae

Ke hōʻike ʻia kahi hōʻike o ka ʻōnaehana hopohopo (hōʻike neurologic):

• ʻO Dementia e hele nei i ka maikaʻi
• Ke hele wāwae paʻakikī
• ʻO ka neʻe ʻana o nā maka i kaupalena ʻia
• ʻIke maʻamau, hoʻolohe, manaʻo, a me ka kaohi o ka neʻe
• ʻO nā neʻe paʻakikī a me nā uncoordinated e like me nā maʻi o Parkinson

Hiki i ka mea mālama ola ke hana i nā hōʻike aʻe e hōʻoki i nā maʻi ʻē aʻe:

• Mākēneki resonance kiʻi (MRI) paha e hōʻike shrinking o ka brainstem (hummingbird hōʻailona)
• ʻO ka scan PET o ka lolo e hōʻike i nā loli i mua o ka lolo

ʻO ka pahuhopu o ka mālama ʻana e kaohi i nā ʻōuli. ʻAʻohe lāʻau i ʻike ʻia no PSP.

Hiki ke hoʻāʻo ʻia nā lāʻau e like me levodopa. Hoʻonui kēia mau lāʻau i ka pae o kahi kemika lolo i kapa ʻia ʻo dopamine. Pili ka Dopamine i ka kaohi o ka neʻe. Hiki i nā lāʻau ke hōʻemi i kekahi mau hōʻailona, ​​e like me nā lālā paʻa a i ʻole nā ​​neʻe lohi no kekahi manawa. Akā ʻaʻole maʻa mau lākou e like me ka maʻi o Parkinson.

Pono nā poʻe he nui me PSP i ka mālama a me ka nānā ʻana i ka uaki ke nalowale nā ​​hana o ka lolo.

Hiki i ka mālama ʻana i kekahi manawa ke hōʻemi i nā hōʻailona no kekahi manawa, akā e ʻoi aku ka maikaʻi o ke ʻano. E emi ka hana o ka lolo ma mua o ka manawa. Kū pinepine ka make ma 5 a 7 mau makahiki.

Ke aʻo ʻia nei nā lāʻau hou e mālama ai i kēia ʻano.

Pākuʻi ʻia nā pilikia o PSP:

• ʻO ke kōkō ʻana o ke koko i nā veins (deep vein thrombosis) ma muli o ka palena iki o ka neʻe
• Ka ʻeha mai ka hāʻule ʻana
• Ka nele o ka kaohi i ka hihiʻo
• ʻO ka nalowale o ka lolo ke hana i ka manawa
• Poniaʻi no ka pilikia i ka ale ʻana
• Kaʻai maikaʻi ʻole (malnutrisi)
• Nā hopena ʻaoʻao mai nā lāʻau

Kāhea i kāu mea hāʻawi inā hāʻule pinepine ʻoe, a inā he ʻāʻī kou kino / kino, a me nā pilikia ʻike.

Eia kekahi, e kāhea inā ua ʻike ʻia kahi mea aloha me PSP a ua hōʻole ke ʻano a ʻaʻole hiki iā ʻoe ke mālama hou i ke kanaka ma ka home.

Dementia - nuchal dystonia; Richardson-Steele-Olszewski maʻi; Palsy - supranuclear holomua

• ʻŌnaehana ʻōnaehana waena a me ka ʻōnaehana ʻōnaehana peripheral

ʻO Jankovic J. Parkinson maʻi a me nā ʻano neʻe ʻē aʻe. I: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, eds. ʻO Bradley's Neurology i ka hana lapaʻau. ʻEpekema 7 Piladelapia, PA: Elsevier; 2016: chap 96.

Ling H. ʻO ke ʻano lapaʻau i ka palsy supranuclear holomua. J Mov Disord. 2016; 9 (1): 3-13. PMID: 26828211 pubmed.ncbi.nlm.nih.gov/26828211/.

Pūnaewele National Institute of Neurological Disorder. Pepa ʻoiaʻiʻo supranuclear holomua. www.ninds.nih.gov/Disorders/Patient-Caregiver-Education/Fact-Sheets/Progressive-Supranuclear-Palsy-Fact-Sheet. Hoʻohou ʻia Malaki 17, 2020. Loaʻa iā ʻAukake 19, 2020.