Polycythemia - hānau hou

Hiki i ka Polycythemia ke hana ke nui a nui nā hunaola ʻulaʻula (RBC) i ke koko o kahi pēpē.

ʻO ka pākēneka o nā RBC i ke koko o ke pēpē i kapa ʻia ʻo "hematocrit." Ke ʻoi aku kēia ma mua o 65%, aia ka polycythemia.

Hiki i ka Polycythemia ke hopena mai nā kūlana e hoʻomohala ma mua o ka hānau ʻana. Pākuʻi ʻia kēia mau mea:

• Lohi i ka hoʻopaʻa ʻana i ka umbilical cord
• ʻO ka maʻi diabetes i ka makuahine hānau o ka pēpē
• Nā maʻi i hoʻoilina ʻia a me nā pilikia kūpuna
• ʻOi aku ka liʻiliʻi o ka oxygen i ke kino (hypoxia)
• Twin-māhoe transfusion maʻi pale (ia ll when ke koko e neʻe mai kekahi māhoe i kekahi)

Hiki i nā RBC keu ke hoʻolohi a pale paha i ke kahe o ke koko i nā kīʻaha koko liʻiliʻi loa. Kapa ʻia kēia ʻo hyperviscosity. Hiki i kēia ke alakaʻi i ka make o ke kino mai ka nele o ka oxygen. Hiki i kēia kahe o ke kahe ke hoʻopili i nā mea āpau, e like me nā puʻupaʻa, nā akemāmā, a me ka lolo.

Pākuʻi ʻia paha nā ʻōuli:

• Hiamoe nui loa
• Nā pilikia hānai
• Ka hopu ʻana i nā maʻi

Aia paha he mau hōʻailona o nā pilikia hanu, maikaʻi ʻole o ka puʻupaʻa, kō kō kō, a i ʻole jaundice hānau hou.

Inā loaʻa nā ʻōuli o ka pēpē i ka hyperviscosity, e hana ʻia kahi hōʻike koko e helu i ka helu o nā RBC. Kapa ʻia kēia hōʻoia he hematocrit.

Hiki i nā hoʻokolohua ʻē aʻe ke:

• ʻO nā kinoea koko e nānā i ka pae o ka oxygen i loko o ke koko
• ʻO ke kō kō (glucose) e nānā ai i ke kō kō kō
• ʻO ka nitrogen urea koko (BUN), kahi mea hana ke wāwahi ka protein
• ʻĀiwi
• Urinalysis
• Bilirubin

E kiaʻi ʻia ka pēpē no nā pilikia o hyperviscosity. Hiki ke hāʻawi ʻia nā wai ma o ka aa. Hana ʻia kekahi transfusion pāʻālua hoʻololi i kekahi manawa i kekahi mau manawa. Eia nō naʻe, ʻaʻole ʻike iki ʻia ka maikaʻi o kēia. He mea nui ia e mālama i ke kumu kumu o ka polycythemia.

Maikaʻi ka kuanaʻike no nā pēpē me ka hyperviscosity akahai. Hiki nō hoʻi nā hopena maikaʻi i nā pēpē i loaʻa ka lāʻau no ka hyperviscosity koʻikoʻi. E nānā ka nānā i ke kumu o ke ʻano.

Hiki paha i kekahi mau keiki ke loaʻa i nā loli hoʻomohala mālie. Pono nā mākua e hoʻopili aku i kā lākou kahu mālama ola inā manaʻo lākou e hōʻike ana kā lākou keiki i nā hōʻailona o ka lohi o ka hoʻomohala.

Komo pū nā pilikia:

• Ka make ʻana o kaʻiʻo ʻōpū (nekrotizing enterocolitis)
• Hoʻoemi i ka mana kaʻa maikaʻi
• Hewa ʻole nā ​​hakuʻala
• Ka hopu ʻana i nā maʻi
• Hahau

Polycythemia hānau hou; Hyperviscosity - hānau hou

• Nā pūnaewele koko

ʻO Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM. Nā maʻi koko. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 124.

Letterio J, Pateva I, Petrosiute A, Ahuja S. Hematologic a me nā pilikia oncologic i ka fetus a neonate. I: Martin RJ, Fanaroff AA, Walsh MC, hua. ʻO Fanaroff lāua ʻo Martin's Neonatal-Perinatal Medicine. 11th hua. Piladelapia, PA: Elsevier; 2020: chap 79.

Tashi T, Prchal JT. ʻO Polycythemia. I: Lanzkowsky P, Lipton JM, Fish JD, eds. ʻO Lanzkowsky's Manual of Pediatric Hematology a me Oncology. ʻElua huaʻōlelo Cambridge, MA: Elsevier Academic Press; 2016: chap 12.