Amyloidosis hoʻoilina
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ʻO ka amyloidosis hereditary kahi kūlana kahi e waiho ai nā waihona protein ʻino (i kapa ʻia ʻo amyloid) i loko o nā kino āpau i ke kino. Hoʻokomo pinepine nā waihona hōʻino i ka puʻuwai, nā puʻupaʻa, a me nā ʻōnaehana. Hoʻopōʻino kēia mau waihona protein i nāʻaʻaʻa a hoʻopilikia i ka hana ʻana o nā meaola.
Ua hoʻoili ʻia ka amyloidosis hoʻoilina mai nā mākua i kā lākou keiki (hoʻoilina). He pāʻani paha kā Genes i ka amyloidosis mua.
ʻAʻole hoʻoilina nā ʻano amyloidosis ʻē aʻe. Pākuʻi ʻia lākou:
- ʻŌnaehana Senile: ʻike ʻia i ka poʻe ma mua o 70
- Kūpono ʻole: hana ʻia me ke kumu ʻole i ʻike ʻia
- Secondary: nā hopena mai nā maʻi e like me ke kanesa o nā huna koko (myeloma)
Nā kūlana kikoʻī nā:
- Amyloidosis Cardiac
- Cerebral amyloidosis
- Amyloidosis ʻōnaehana lua
ʻO ka mālama ʻana e hoʻomaikaʻi i ka hana o nā mea i hōʻino ʻia e kōkua i ka hōʻoluʻolu i kekahi mau ʻōuli o ka amyloidosis hoʻoilina. Hiki ke kōkua i kahi loli ate e hōʻemi i ka hana ʻana o nā protein amyloid weliweli. E kamaʻilio me kāu mea mālama ola e pili ana i nā lāʻau lapaʻau.
ʻO Amyloidosis - hoʻoilina hoʻoilina; Amyloidosis ʻohana
ʻO Amyloidosis o nā manamana lima
Budd RC, Seldin DC. ʻO Amyloidosis. I: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, nā hua. ʻO Kelley lāua ʻo Firestein's Bookbook of Rheumatology. 10 o ka lā. Piladelapia, PA: Elsevier; 2017: chap 116.
ʻO Gertz MA. ʻO Amyloidosis. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 179.
ʻO Hawkins PN. ʻO Amyloidosis. I: Hochberg MC, Gravallese EM, Silman AJ, Smolen JS, Weinblatt ME, Weisman MH, eds. Rheumatology. ʻEpekema 7 Piladelapia, PA: Elsevier; 2019: chap 177.