Fanconi maʻi maʻi

Anter

• Nā ʻōuli o Fanconi Syndrome
• Ka mālama ʻana i ka Fanconi Syndrome
• Loulou pono:

ʻO Fanconi Syndrome kahi maʻi maʻamau o nā puʻupaʻa e alakaʻi i ka hōʻiliʻili ʻana o ka glucose, bicarbonate, potassium, phosphates a me kekahi mau amino acid i loko o ka mimi. I kēia maʻi he nalowale pū kekahi o ka protein i ka mimi a lilo ka mimi i ikaika a ʻoi aku ka waikawa.

Hoʻokumu ʻo Hereditary Fanconi Syndrome i nā hoʻololi kūʻē i hoʻoili ʻia mai ka makuakāne a ke keiki. I ka hihia o Loaʻa iā Fanconi Syndrome, kaʻai ʻana i nā metala kaumaha, e like me ke kēpau, ka ʻai ʻana i nā lāʻau ʻaloʻalo pau ʻole, ka lawa ʻole o ka wikamina D, ka hoʻoneʻe ʻana o nā puʻupaʻa, nā myeloma maha a i ʻole amyloidosis i hiki ke alakaʻi ʻia i ka maʻi.

ʻAʻohe lāʻau lapaʻau ʻo Fanconi Syndrome a ʻo kāna lapaʻau ʻana ka hakahaka o ka hoʻololi ʻana i nā mea i nalowale i ka mimi, i kuhikuhi ʻia e ka nephrologist.

Nā ʻōuli o Fanconi Syndrome

ʻO nā ʻōuli o Fanconi Syndrome hiki ke:

• Urencing nui o ka mimi;
• Mimi ikaika a me ka acidic;
• Make wai loa;
• Make wai;
• Pōkole;
• ʻO ka acidity kiʻekiʻe i ke koko;
• Nāwaliwali;
• ʻEha iwi;
• Nā pākuʻi waiū kope-waiū ma ka ʻili;
• Ka loaʻa ʻole a kīnā ʻole i nā manamana nui;

Maʻamau, ʻano o Fanconi Syndrome ʻike ʻia ka hoʻoilina i ka wā kamaliʻi ma kahi o 5 mau makahiki.

ʻ ʻike o Fanconi Syndrome hana ʻia ia ma muli o nā ʻōuli, kahi hoʻāʻo koko e hōʻike ana i ka kiʻekiʻe acidity a me kahi hōʻike mimi e hōʻike ana i ka nui o ka glucose, phosphate, bicarbonate, uric acid, potassium a me ka sodium.

Ka mālama ʻana i ka Fanconi Syndrome

Hoʻolālā ka mālama ʻana o Fanconi Syndrome e hoʻohui i nā mea i nalowale e kekahi kanaka i ka mimi. No kēia, pono paha i nā mea maʻi e lawe i ka pāhare potassium, phosphate a me ka vitamina D, a ʻo ka sodium bicarbonate e hoʻopau i ka acidosis koko.

I nā mea maʻi me ka hōʻeha loa o ka puʻuwai, hōʻike ʻia ke transplantation kidney.

Loulou pono:

• Nā meaʻai waiwai potassium
• Nā meaʻai e waiwai i ka wikamina D

• Ke hoʻoliʻiliʻi hakuʻala