Neutropenia - pēpē
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ʻO Neutropenia kahi helu haʻahaʻa haʻahaʻa o nā hunaola keokeo. Kapa ʻia kēia mau hunaola neutrophil. Kōkua lākou i ke kino e hakakā i ka maʻi. Kūkākūkā kēia ʻatikala i ka neutropenia i nā keiki hānau hou.
Hana ʻia nā hunaola keʻokeʻo i ka momona o ka iwi. Hoʻokuʻu ʻia lākou i ke kahe o ke koko a hele i nā wahi a lākou e pono ai. Kū nā pae haʻahaʻa o nā neutrophil ke hiki ʻole i ka iwi iwi ke pani iā lākou i ka wikiwiki e pono ai.
I nā pēpē, ʻo ka maʻi ka kumu maʻamau. ʻO kahi maʻi ʻino loa ke kumu e hoʻohana koke ʻia nā neutrophil. Hiki iā ia ke pale i ka momona o ka iwi mai ka hana ʻana i nā neutrophil hou aku.
I kekahi manawa, ʻo ka pēpē maʻi ʻole ka helu neutrophil haʻahaʻa no ke kumu ʻole. ʻO kekahi mau maʻi i ka makuahine hāpai, e like me preeclampsia, hiki ke alakaʻi i ka neutropenia i nā pēpē.
I nā hihia maʻamau, loaʻa paha i nā mākuahine nā mea pale e kūʻē i nā neutrophil o kā lākou pēpē. Keʻa nei kēia mau antibodies i ka placenta ma mua o ka hānau ʻana a haki nā hunaʻi o ke pēpē (alloimmune neutropenia). I nā hihia ʻano ʻē aʻe, hiki i kahi pilikia me ka iwi iwi o ka pēpē ke alakaʻi i ka hōʻemi ʻana i ka hana keokeo o ke koko.
E hoʻouna ʻia kahi mea liʻiliʻi o ke koko o ka pēpē i ke keʻena hoʻokolohua no kahi helu piha o ke koko (CBC) a me ka hoʻokaʻawale ʻana o ke koko. Hōʻike kahi CBC i ka helu a me ke ʻano o nā hunaola i loko o ke koko. Kōkua ka mea ʻokoʻa i ka helu o nā ʻano ʻokoʻa o nā hunaola keokeo i kahi hāpana koko.
Pono e loaʻa a mālama ʻia ke kumu o kekahi maʻi.
I nā manawa he nui, hele aku ʻo neutropenia iā ia iho e like me ka hoʻihoʻi ʻana o ka iwi iwi a hoʻomaka i ka hana ʻana i lawa nā keʻokeʻo koko keʻokeʻo.
I nā kūlana kūleʻa ke haʻahaʻa ka helu neutrophil e hoʻoweliweli i ke ola, e ʻōlelo ʻia nā ʻano aʻe aʻe:
- Nā lāʻau e hoʻonāukiuki i ke keʻokeʻo o ke koko
- Nā Antibodies mai nā hāpana koko i hāʻawi manawaleʻa ʻia (intravenous immune globulin)
Pili ka nānā o ka pēpē i ke kumu o ka neutropenia. ʻO kekahi mau maʻi a me nā kūlana ʻē aʻe i nā keiki hānau hou hiki ke hoʻoweliweli i ke ola. Eia naʻe, ʻaʻole pili ka hapa nui o nā maʻi i nā hopena ʻaoʻao lōʻihi ma hope o ka hele ʻana o neutropenia a i ʻole mālama ʻia.
E maikaʻi pū kekahi ʻo Alloimmune neutropenia ke hele aku nā mea ʻē aʻe a ka makuahine mai ke kahe o ke pēpē.
Nā Neutrophil
ʻO Benjamin JT, Torres BA, Maheshwari A. Neonatal leukocyte physiology a me nā maʻi. I: Gleason CA, Juul SE, eds. Nā maʻi o Avery o ke keiki hānau. 10 o ka lā. Piladelapia, PA: Elsevier; 2018: chap 83.
Koenig JM, Bliss JM, Mariscalco MM. ʻO ka physiology neutrophil maʻamau a maʻamau hoʻi i ka hānau hou. I: Polin RA, Abman SH, Rowitch DH, Benitz WE, Fox WW, eds. ʻO Fetal and Neonatal Physiology. 5th lā. Piladelapia, PA: Elsevier; 2017: chap 126.
Nā pilikia ʻo Letterio J, Ahuja S. Hematologic. I: Fanaroff AA, Fanaroff JM, eds. ʻO Klaus lāua ʻo Fanaroff's Care of the High-Risk Neonate. ʻEpekema 7 St Louis, MO: Elsevier; 2020: chap 16.