Mea Kākau: Janice Evans
Lā O Ka Hana: 27 Iulai 2021
HōʻAno Hou I Ka Lā: 10 Mei 2025
Anonim
NEFROCALCINOSIS MEDULAR
Wikiō: NEFROCALCINOSIS MEDULAR

ʻO Nefrocalcinosis kahi maʻi kahi e nui ai ka calcium i waiho ʻia i nā puʻupaʻa. He mea mau ia i nā pēpē ma mua.

ʻO kēlā me kēia maʻi e alakaʻi i nā kiʻekiʻe o ka calcium i ke koko a i ʻole ka mimi e alakaʻi i ka nephrocalcinosis. I kēia maʻi, waiho nā calcium i ke aʻa puʻupaʻa ponoʻī. ʻO ka hapa nui o ka manawa, hoʻopili ʻia nā puʻupaʻa ʻelua.

Pili ʻia ka nezrocalcinosis, akā ʻaʻole like ia me nā pōhaku ʻōiwi (nephrolithiasis).

Nā kūlana i hiki ke hoʻokumu i nephrocalcinosis me:

  • ʻOihana syndome
  • ʻO Bartter Syndrome
  • Glomerulonephritis maʻi
  • ʻO ka hypomagnesemia ʻohana
  • ʻO ke akepaʻa huahuakai medullary
  • Hyperoxaluria kumu
  • Ka hōʻole ʻana i ke transplant renal
  • Renal tubular acidosis (RTA)
  • Nekrosis huakō

ʻO nā kumu kumu ʻē aʻe o nephrocalcinosis me:

  • Ethylene glycol ʻino
  • Hypercalcemia (ʻoi aku ka calcium i ke koko) ma muli o hyperparathyroidism
  • Hoʻohana o kekahi mau lāʻau, e like me acetazolamide, amphotericin B, a me triamterene
  • ʻO Sarcoidosis
  • Tuberculosis o ka hakuʻala a me nā maʻi e pili ana i ka maʻi SIDA
  • ʻO ka lāʻau Vitamin D

ʻO ka hapa nui o ka manawa, ʻaʻohe hōʻailona mua o nephrocalcinosis ma mua o nā ʻano o ke ʻano e hoʻopilikia nei.


Loaʻa paha i ka poʻe i loaʻa nā pōhaku hakuʻala:

  • Koko i ka mimi
  • Fiva a me nā anuanu
  • ʻO Nusea a me ka luaʻi
  • ʻO kaʻeha nui ma ka ʻōpū, nā ʻaoʻao o ke kua (flank), ʻūhū, a i ʻole nā ​​testicle

ʻO nā ʻōuli ma hope e pili ana i ka nephrocalcinosis e pili pū paha me ka holo wā lōʻihi ʻole (mau) ʻole.

Hiki ke ʻike ʻia nā nezrocalcinosis ke loaʻa nā ʻōuli o ka lawa ʻole o ke kōkō, ʻole ka puʻuwai, ka uropathy ālai, a i ʻole nā ​​pōhaku o ka urinary

Hiki i nā hoʻokolohua kiʻi ke kōkua i ke kuhi ʻana i kēia ʻano. ʻO nā hoʻāʻo e hana ʻia ana paha:

  • Scanner CT ʻōpū
  • Ultrasound o ka hakuʻala

Nā hoʻokolohua ʻē aʻe i hiki ke hana ʻia e kuhikuhi a hoʻoholo i ka nui o nā maʻi e pili pū ana me:

  • ʻO nā hoʻokolohua koko e nānā i nā pae o ka calcium, phosphate, uric acid, a me ka hormone parathyroid
  • ʻIke ʻo Urinalysis e ʻike i nā aniani a nānā i nā hunaola ʻulaʻula
  • ʻO ka hōʻiliʻili mimi he 24 mau hola e ana i ka acidity a me nā pae o ka calcium, sodium, uric acid, oxalate, a me citrate

ʻO ka pahuhopu o ka mālama ʻana e hōʻemi i nā hōʻailona a pale i ka nui o ka calcium mai ke kūkulu ʻana i nā puʻupaʻa.


E hoʻopili ka mālama ʻana i nā hana e hōʻemi ai i nā kiʻekiʻe o ka calcium, phosphate, a me oxalate i loko o ke koko a me ka mimi. ʻO nā koho e pili ana i ka hoʻololi ʻana i kāu papaʻai a me ka lawe ʻana i nā lāʻau a me nā mea hoʻopili.

Inā ʻoe e lawe i ka lāʻau e lilo ai ka calcium, e haʻi aku kāu mea mālama ola iā ʻoe e haʻalele i ka lawe ʻana iā ia. Mai hōʻoki i ka lawe ʻana i nā lāʻau i mua o ke kamaʻilio ʻana i kāu mea hāʻawi.

ʻO nā ʻōuli ʻē aʻe, e pili ana i nā pōhaku hakuʻala, pono e mālama ʻia ke kūpono.

Aia ka mea e hilinaʻi ai i nā pilikia a me ke kumu o ka maʻi.

Hiki i ka mālama kūpono ke kōkua i ka pale ʻana i nā waihona hou aʻe i nā puʻupaʻa. I ka hapanui o nā hihia, ʻaʻohe ala e hemo ai i nā waihona i hana mua ʻia. ʻO ka nui o nā waihona o ka calcium i nā puʻupaʻa, ʻaʻole ia e hōʻino nui i nā puʻupaʻa.

Komo pū nā pilikia:

  • Hewa kōwi koʻikoʻi
  • Ka wā lōʻihi (mau) kō ʻole o ke kō
  • Pohaku hakuʻala
  • ʻO uropathy ākea (koʻikoʻi a mau ʻole paha, unilateral a i ʻole ʻelua ʻelua)

Kāhea i kāu mea hāʻawi inā ʻike ʻoe he maʻi kāu e kumu ai i nā kiʻekiʻe o ka calcium i loko o kou koko a me ka mimi. Kāhea pū inā hana ʻoe i nā ʻōuli o nephrocalcinosis.


ʻO ka mālama koke ʻana i nā maʻi e alakaʻi ai i nephrocalcinosis, me RTA, hiki ke pale iā ia mai ka hoʻomohala ʻana. ʻO ka inu ʻana i ka wai he nui e mālama i nā puʻupaʻa a kahe ka wai e kōkua i ka pale ʻana a hōʻemi paha i ka hoʻokumu ʻia ʻana o ka pōhaku.

  • Nā pōhaku hakuʻala - he aha e nīnau aku ai i kāu kauka
  • ʻŌnaehana mimi kāne

Bushinsky DA. Pohaku hakuʻala. I: Melmed S, Auchus, RJ, Goldfine AB, Koenig RJ, Rosen CJ, eds. ʻO Williams Textbook of Endocrinology. 14th ed. Piladelapia, PA: Elsevier; 2020: chap 32.

ʻO Chen W, Monk RD, Bushinsky DA. ʻO Nefrolithiasis a me nephrocalcinosis. I: Feehally J, Floege J, Tonelli M, Johnson RJ, eds. Nā Nephrology Haumāna piha. ʻElua huaʻōlelo Piladelapia, PA: Elsevier; 2019: chap 57.

ʻO Tublin M, Levine D, Thurston W, Wilson SR. ʻO ka hakuʻala a me ka urinary tract. I: Rumack CM, Levine D, eds. ʻIkioma ultrasound. 5th lā. Piladelapia, PA: Elsevier; 2018: chap 9.

ʻO Vogt BA, ʻo Springel T. ʻO ke kīʻaha a me nā wahi urinary o ka neonate. I: Martin RJ, Fanaroff AA, Walsh MC, hua. ʻO Fanaroff lāua ʻo Martin's Neonatal-Perinatal Medicine. 11th hua. Piladelapia, PA: Elsevier; 2020: chap 93.

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