Berdon Syndrome: he aha ia, nā ʻōuli a me nā lāʻau

Anter

• Nā hōʻailona nui
• Pehea e hana ai i ka lāʻau

ʻO Berdon Syndrome kahi maʻi maʻi laha ʻole e pili nui i nā kaikamahine a hana i nā pilikia i loko o ka ʻōpū, ʻōpū a me ka ʻōpū. ʻO ka maʻamau, ʻaʻole pīpī a poop paha nā poʻe me kēia maʻi a pono e hānai ʻia e ka paipu.

Hiki ke kumu ʻia kēia maʻi e nā pilikia genetical a i ʻole hormonal a hōʻike koke ʻia nā ʻōuli ma hope koke o ka hānau ʻana, kahi hiki ke loli i ke kinona a me ka hana o ka puhā, kahi nui loa, hoʻoliʻiliʻi a hele ʻole paha nā ʻōpū, a hiki i ka hopu ʻia o ka ʻōpū. , me ka hoʻoliʻiliʻi o ka nui o ka ʻōpū nui a me ka pehu ʻana o ka ʻōpū liʻiliʻi.

ʻAʻohe lāʻau o Berdon Syndrome, akā aia kekahi mau kaʻina hana e kuhi ai e wehe i ka ʻōpū a me nā ʻōpū, hiki ke hoʻomaikaʻi i nā ʻōuli o ka maʻi. Hoʻohui ʻia, kahi koho ʻē aʻe e hoʻonui i ke ola o ke kanaka me ka maikaʻi o kēia kanaka me kēia maʻi ka transplantation multivisceral, ʻo ia hoʻi, ka transplantation o ka ʻōnaehana gastrointestinal holoʻokoʻa.

Nā hōʻailona nui

Hōʻike ʻia nā ʻōuli o Berdon syndrome ma hope koke iho o ka hānau ʻana, ʻo nā mea nui:

• Puʻupuʻu;
• Paʻa mimi;
• Pākuʻi dilated;
• Pehu o ka ʻōpū;
• Palupalu nā mākala o ka ʻōpū;
• ʻO ka luaʻi;
• ʻŌpuʻu ʻōhū;
• Pāpale ʻōpū.

Hoʻomaopopo ʻia ke kuhi o Berdon's Syndrome e ke ana ʻana i nā ʻōuli i hōʻike ʻia e ke keiki ma hope o ka hānau ʻana a me nā hoʻokolohua kiʻi ʻana, e like me ultrasound. Hiki ke ʻike ʻia ka maʻi i ka wā hāpai ma o ka hana ʻana i nā ultrasound morphological ma hope o ka hebedoma 20 o ka hāpai keiki. Hoʻomaopopo i ke aha no ka ultrasound morphological.

Pehea e hana ai i ka lāʻau

ʻAʻole hiki i ka mālama ʻana iā Berdon Syndrome ke hāpai i ka hoʻōla o ka maʻi, akā kōkua ia i ka hōʻemi ʻana i nā hōʻailona ma nā mea maʻi a hoʻomaikaʻi i ko lākou ola.

Paipai ʻia ke ʻoki kino ʻana i ka ʻōpū a i ʻole ka ʻōpū e unclog i kēia mau lālā a hoʻomaikaʻi i kā lākou holo ʻana. Pono e hānai ʻia ka hapa nui o nā mea maʻi ma o ka paipu ma muli o ka pilikia o ka ʻōnaehana digestive. E ʻike pehea e hana ʻia ai ka hānai paipu.

He mea maʻamau nō ke ʻoki ʻana ma luna o ka puhā, e pili ana i ka ʻili ma ka ʻōpū, e ʻae ai ka mimi.

Eia nō naʻe, ʻaʻole pili iki kēia mau kaʻina hana i ka mea hoʻomanawanui, e alakaʻi pinepine ai i ka make mai kaʻai pono ʻole ʻana, nā hanana maha ʻole a me nā maʻi āpau i loko o ke kino, sepsis. No kēia kumu, ua lilo ka transplantation multivisceral i koho koho ʻoi loa a me nā hana ʻelima i ka manawa hoʻokahi: transplantation of ʻōpū, duodenum, ʻōpū, pancreas a me ke ake.