ʻO ka pilina ma waena o Exocrine Pancreatic Insufficiency a me Cystic Fibrosis

Anter

• He aha ke kumu o ka cystic fibrosis?
• He aha nā mea pilikia no ka cystic fibrosis?
• Pehea e pili ai ʻo EPI a me cystic fibrosis?
• He aha nā ʻano hana i loaʻa no EPI?
• Lawe ʻia

ʻO Cystic fibrosis kahi maʻi i hoʻoili ʻia e kumu i nā wai o ke kino e mānoanoa a pili hoʻi ma kahi o ka lahilahi a me ka holo. Hoʻopili kēia i nā māmā a me ka ʻōnaehana digestive.

Loaʻa ka pilikia o ka hanu i ka poʻe me ka cystic fibrosis ma muli o ke kūpē ʻana o ka mucus i ko lākou mau māmā a hoʻoweliweli iā lākou i nā maʻi. Hoʻopili pū nā mākala mānoanoa i ka pancreas a pale i ka hoʻokuʻu ʻana o nā enzyme digestive. Ma kahi o 90 pākēneka o ka poʻe me ka cystic fibrosis e hoʻomohala pū kekahi i ka insrequence pancreatic exocrine (EPI).

E hoʻomau i ka heluhelu e aʻo hou aʻe e pili ana i ka pilina ma waena o kēia mau ʻano ʻelua.

He aha ke kumu o ka cystic fibrosis?

Hoʻokumu ʻia ʻo Cystic fibrosis e kahi kīnā ma ka ʻaoʻao CFTR. Hoʻohuli ʻia kahi hoʻololi i kēia gen i kumu e hana ai nā hunaola i nā wai mānoanoa. ʻO ka hapa nui o ka poʻe me ka cystic fibrosis e ʻike ʻia i ka wā ʻōpio.

He aha nā mea pilikia no ka cystic fibrosis?

ʻO Cystic fibrosis kahi maʻi maʻi. Inā loaʻa ka maʻi i kou mau mākua a i ʻole inā lawe lākou i ka ʻāpana hemahema, aia ʻoe i ka nui o ka makaʻu no ka hoʻomohala ʻana i ka maʻi. Pono i kahi kanaka me ka cystic fibrosis e hoʻoilina i ʻelua mau genes mutated, hoʻokahi mai kēlā me kēia makua. Inā lawe wale ʻoe i hoʻokahi kope o ka moʻokūʻauhau, ʻaʻohe ou cystic fibrosis akā he hāpai ʻoe i ka maʻi. Inā loaʻa he keiki i nā mea lawe ʻelua, aia he 25 pākēneka loaʻa i kā lākou keiki ke loaʻa i ka cystic fibrosis. Aia kahi 50 pakeneka kūpono e lawe kā lākou keiki i ka ʻāpana akā ʻaʻohe cystic fibrosis.

ʻOi aku ka maʻamau o ka cystic fibrosis i ka poʻe o ko ka ʻĀkau ʻEulopa.

Pehea e pili ai ʻo EPI a me cystic fibrosis?

ʻO EPI kahi pilikia nui o cystic fibrosis. ʻO Cystic fibrosis ka lua o nā kumu maʻamau o EPI, ma hope o ka pancreatitis mau. Kū ʻia ia no ka mea ʻo ka mumū mānoanoa i kāu pancreas e ālai i nā enzyme pancreatic mai ke komo ʻana i ka ʻōpū liʻiliʻi.

ʻO ka nele o nā enzyme pancreatic i ke ʻano o ka hele ʻana o ka digestive tract i ka meaʻai i hoʻoiho ʻole ʻia. He paʻakikī nā momona a me nā protein i nā poʻe me EPI e ʻeli.

Kēia hapa digestion a me ka omo o ka ai ke alakaʻi i:

• abdominal eha
• ʻōhūhū
• kōpaʻa
• pāhoehoe
• nā noho momona a palu
• Kaumaha emi
• hana maikaʻi ʻole

ʻOiai ʻoe e ʻai i ka nui o nā meaʻai, hiki i ka cystic fibrosis ke paʻakikī i ka mālama ʻana i kahi kaupaona olakino.

He aha nā ʻano hana i loaʻa no EPI?

Hiki i ke ʻano olakino olakino a me nā meaʻai kaulike ke kōkua iā ʻoe e hoʻokele i kāu EPI. ʻO kēia ke kaupalena ʻana i ka lawe ʻana i ka wai ʻona, ka hōʻalo ʻana i ka puhipaka, a me ka ʻai ʻana i kahi papaʻai momona me ka nui o nā mea kanu a me nā hua nui. Hiki i ka hapanui o ka poʻe me ka cystic fibrosis ke ʻai i kahi papaʻai maʻamau kahi e hele ai ka 35 a 45 mau pākēneka o nā calorie mai ka momona.

Pono ʻoe e lawe i nā panaʻi énima me kāu mau meaʻai āpau a me nā meaʻai māmā e hoʻomaikaʻi ai i ka digestion. Hiki ke kōkua i ka hoʻohana supplementation no ka hana ʻana i nā wikamina e pale aku ai ʻo EPI i kou kino mai ke komo ʻana.

Inā hiki ʻole iā ʻoe ke mālama i kahi kaupaona olakino, manaʻo paha kāu kauka e hoʻohana ana i ka paipu hānai i ka pō e pale ai i ka hōʻino kino mai EPI.

He mea nui i kāu kauka e nānā i kāu hana pancreatic, ʻoiai inā ʻaʻole ʻoe i hoʻemi i ka hana no ka mea hiki ke hōʻole i ka wā e hiki mai ana. ʻO ka hana ʻana pēlā e hoʻokele ai i kou kūlana a hiki ke hoʻohaʻahaʻa i kou manawa e hōʻeha hou aku ai i kāu pancreas.

Lawe ʻia

I ka wā ma mua, ʻo ka poʻe me ka cystic fibrosis he mau manaʻolana pōkole loa ko lākou. I kēia lā, 80 pākēneka o ka poʻe me ka cystic fibrosis hiki i ka makua. ʻO kēia no nā holomua nui i ka mālama ʻana a me ka mālama ʻana i nā ʻōuli. No laila ʻoiai ʻaʻohe lāʻau lapaʻau no ka cystic fibrosis, nui ka manaolana.